脑膜-额-鼻-眶-上颌复合部血管外皮细胞瘤。
Hemangiopericytoma of meningo-fronto-naso-orbito-maxillary complex.
机构信息
Oral and Maxillofacial Surgery, Government Dental College, Indore, India.
Dentistry, All India Institute of Medical Science, Bhopal, India
出版信息
BMJ Case Rep. 2020 Oct 4;13(10):e239135. doi: 10.1136/bcr-2020-239135.
Hemangiopericytoma (HPC) is a rare vascular tumour and difficult to diagnose clinically. Incidence is reported in fourth to fifth decade of life.With female predominance, 3%-5% cases affect the oral cavity, sinus lining and meninges. The patient presented with 8×6 cm swelling on her face, evaluation reported it to be HPC. Bilateral maxillary artery embolisation, wide local excision of the lesion, preserving the left eye and its function, was done. No recurrence is reported at 1-year follow-up. Response of such lesions to radiotherapy is questionable; with no lymphadenopathy and adequate encapsulation, embolisation of feeder vessel followed by a wide local excision of the lesion seems to be a fairly good option of treatment.
血管外皮细胞瘤（HPC）是一种罕见的血管肿瘤，临床诊断困难。发病率报道为第四至第五个十年。女性多见，3%-5%的病例累及口腔、鼻窦内衬和脑膜。患者面部出现 8×6cm 的肿胀，评估报告为 HPC。行双侧上颌动脉栓塞、病变广泛切除，保留左眼及其功能。1 年随访无复发。此类病变对放疗的反应存在争议；无淋巴结病和充分包膜，栓塞供血血管后行病变广泛切除术似乎是一种相当不错的治疗选择。
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