Chow Pak-Cheong, Rocha Barnabe A, Au Timmy W K, Yung Tak-Cheung
Department of Paediatric Cardiology, Queen Mary Hospital, Hong Kong Special Administrative Region.
Department of Cardiothoracic Surgery, Queen Mary Hospital, Hong Kong Special Administrative Region.
J Cardiol Cases. 2020 Aug 6;22(4):174-176. doi: 10.1016/j.jccase.2020.06.009. eCollection 2020 Oct.
Aortic dilation has been increasingly recognized in congenital heart diseases, and aortic dissection is one of the important complications. We report a case of aortic dissection in a patient 31 years after repair of tetralogy of Fallot (TOF) and review reported cases. While aortic dissection is uncommon, aortic dilation is common among patients with repaired TOF and it appeared progressive in some patients. Based on the reported cases, progressive aortic dilation appeared as the pre-requisite for aortic dissection, although other factors might be involved. Regular surveillance and monitoring for aortic complications should be incorporated into clinical practice. < Aortic dilation is common but aortic dissection is uncommon in patients with tetralogy of Fallot, and threshold for prophylactic surgery is lacking. Recognition of progressive aortic dilation is important to identify patients at risk of aortic dissection in tetralogy of Fallot.>.
主动脉扩张在先天性心脏病中越来越受到重视，主动脉夹层是其重要并发症之一。我们报告1例法洛四联症（TOF）修复术后31年发生主动脉夹层的病例，并回顾已报道的病例。虽然主动脉夹层并不常见，但主动脉扩张在TOF修复术后患者中很常见，且在一些患者中呈进行性发展。根据已报道的病例，尽管可能涉及其他因素，但进行性主动脉扩张似乎是主动脉夹层的先决条件。临床实践中应纳入对主动脉并发症的定期监测。<主动脉扩张在法洛四联症患者中常见，但主动脉夹层不常见，且缺乏预防性手术的阈值。认识到进行性主动脉扩张对于识别法洛四联症患者发生主动脉夹层的风险很重要。>
