Pediatric Surgery Department. La Misericordia Pediatric Hospital Foundation. Colombia National University. Bogotá (Colombia).
Pediatric Radiology Department. La Misericordia Pediatric Hospital Foundation. Colombia National University. Bogotá (Colombia).
Cir Pediatr. 2020 Oct 1;33(4):177-182.
Pancreaticobiliary maljunction (PBM) is a congenital malformation characterized by a long common pancreaticobiliary channel which causes sphincter of Oddi malfunction. In children, it is typically diagnosed using magnetic resonance cholangiopancreatography (MRCP). It is associated with congenital biliary dilatation, pancreatitis, and gallbladder and bile duct tumors at adulthood. Studies in the western population are rare. Given its morbidity rate, it should be searched for in the western pediatric population. The objective of this study was to look for and identify the presence of pancreaticobiliary maljunction through MRCP in pediatric patients with biliary or pancreatic disease, as well as to find out other associated factors.
MRCP was used to measure common channel length, pancreatic duct length, and bile duct diameter in 41 pediatric patients with biliary or pancreatic disease.
The common channel could only be measured in 17.6% of cases, 50% of which were >8 mm long. All patients were female and had congenital biliary dilatation. No age-related differences were found in terms of bile duct length.
PBM is present in the western pediatric population, but prevalence and morbidity are unknown. Larger studies are required to identify morbidity and mortality, as well as prevalence among patients.
胰胆管合流异常（PBM）是一种先天性畸形，其特征为胰胆管共同通道较长，导致Oddi 括约肌功能障碍。在儿童中，通常使用磁共振胆胰管成像（MRCP）进行诊断。它与先天性胆管扩张、胰腺炎以及成年后患胆囊和胆管肿瘤有关。在西方人群中的研究较少。鉴于其发病率，应在西方儿科人群中进行筛查。本研究的目的是通过 MRCP 在患有胆胰疾病的儿科患者中寻找和确定胰胆管合流异常的存在，并找出其他相关因素。
对 41 例患有胆胰疾病的儿科患者进行 MRCP 以测量共同通道长度、胰管长度和胆管直径。
仅能测量 17.6%的病例的共同通道，其中 50%长度>8mm。所有患者均为女性，患有先天性胆管扩张。胆管长度无年龄相关差异。
PBM 存在于西方儿科人群中，但患病率和发病率尚不清楚。需要进行更大规模的研究以确定发病率和死亡率以及患者中的患病率。
