Lee Chang-Ha, Lim Jae Hong, Kim Eung Rae, Kim Yong Jin
Department of Thoracic and Cardiovascular Surgery, Sejong General Hospital, Bucheon, Korea.
Korean J Thorac Cardiovasc Surg. 2020 Oct 5;53(5):243-249. doi: 10.5090/kjtcs.20.113.
Ebstein anomaly is a rare congenital heart malformation typically involving the tricuspid valve and the right ventricle that has a wide range of anatomical and pathophysiological presentations. Various surgical repair techniques for Ebstein anomaly have been reported because of its near-infinite anatomical variability. Cone repair for Ebstein anomaly can achieve nearly anatomical reconstruction of the tricuspid valve with promising outcomes. In this article, the surgical techniques for cone repair in adult patients with Ebstein anomaly are described in detail, and clinical experiences and technically challenging cases are presented.
埃布斯坦畸形是一种罕见的先天性心脏畸形,通常累及三尖瓣和右心室,具有广泛的解剖学和病理生理学表现。由于其解剖结构几乎具有无限的变异性,已有多种针对埃布斯坦畸形的手术修复技术被报道。埃布斯坦畸形的圆锥修复术可实现三尖瓣近乎解剖学的重建,效果良好。本文详细描述了成年埃布斯坦畸形患者圆锥修复术的手术技巧,并介绍了临床经验和技术上具有挑战性的病例。