Sekito Sho, Nishikawa Kohei, Kageyama Takumi, Higashi Shinichirou, Miki Manabu, Kato Manabu, Masui Satoru, Yoshio Yuko, Hasegawa Yoshihiro, Kanda Hideki, Arima Kiminobu, Sugimura Yoshiki
Department of Nephro-Urologic Surgery and Andrology, Mie University Graduate School of Medicine.
Nihon Hinyokika Gakkai Zasshi. 2019;110(4):244-248. doi: 10.5980/jpnjurol.110.244.
A 47-year-old female presented to a clinic complaining of right back pain. A CT scan revealed a right retroperitoneal mass and she was referred to our department for further evaluation. Contrast-enhanced CT and MRI revealed a right retroperitoneal mass (6 cm) in the hilum of the right kidney that invaded the right renal vein and inferior vena cava (IVC). Suspecting a tumor arising from retroperitoneal tissues involving the right renal vein and IVC, the decision was made to excise the tumor with the right kidney, renal vein, and a portion of the IVC. The histologic findings indicated that the tumor was a leiomyosarcoma originating from the renal vein wall. The tumor cells were spindle-shaped and stained positive for desmin, caldesmon and HHF35. The post-operative course was uneventful and she was recurrence-free 20 months after surgery. In addition to presenting a case of a leiomyosarcoma of the renal vein, a short review of the literature is provided.
一名47岁女性到诊所就诊，主诉右背部疼痛。CT扫描显示右腹膜后肿块，她被转诊至我科做进一步评估。增强CT和MRI显示右肾门处有一个6厘米的右腹膜后肿块，侵犯了右肾静脉和下腔静脉（IVC）。怀疑是起源于腹膜后组织并累及右肾静脉和IVC的肿瘤，决定切除肿瘤及右肾、肾静脉和部分下腔静脉。组织学检查结果表明，该肿瘤是起源于肾静脉壁的平滑肌肉瘤。肿瘤细胞呈梭形，结蛋白、钙调蛋白和HHF35染色呈阳性。术后过程顺利，术后20个月无复发。除了介绍一例肾静脉平滑肌肉瘤病例外，还对文献进行了简要综述。
