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Unusual Case of Disseminated Amyloidosis in a Man in His 30s Presenting as Coagulopathy, Recurrent Pancreatitis, and Acute Kidney Injury.

作者信息

Vanga Amaresh, Cousins Ryan, Anjum Malik, Malhotra Varun

机构信息

Eastern Virginia Medical School, Norfolk, VA.

Emory University, Atlanta, GA.

出版信息

Kidney Med. 2020 Aug 7;2(5):667. doi: 10.1016/j.xkme.2020.07.003. eCollection 2020 Sep-Oct.

DOI:10.1016/j.xkme.2020.07.003
PMID:33089145
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7568063/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/e1e0a3d0b266/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/0cafbd4a28ac/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/2792ba7d6df2/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/e1e0a3d0b266/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/0cafbd4a28ac/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/2792ba7d6df2/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4c35/7568063/e1e0a3d0b266/gr3.jpg

相似文献

1
Unusual Case of Disseminated Amyloidosis in a Man in His 30s Presenting as Coagulopathy, Recurrent Pancreatitis, and Acute Kidney Injury.一名30多岁男性患播散性淀粉样变性的罕见病例,表现为凝血病、复发性胰腺炎和急性肾损伤。
Kidney Med. 2020 Aug 7;2(5):667. doi: 10.1016/j.xkme.2020.07.003. eCollection 2020 Sep-Oct.
2
An autopsy case of Reye's syndrome associated with acute pancreatitis, acute renal failure and disseminated intravascular coagulopathy.1例与急性胰腺炎、急性肾衰竭及弥散性血管内凝血相关的瑞氏综合征尸检病例
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Fatal acute pancreatitis with cystic formation in reactive systemic AA amyloidosis secondary to rheumatoid arthritis.类风湿关节炎继发反应性全身性AA淀粉样变性伴囊性形成的致命性急性胰腺炎。
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J Nephrol. 2006 May-Jun;19(3):361-5.
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Fatal pancreatitis associated with systemic amyloidosis in a rheumatoid arthritis patient.一名类风湿关节炎患者发生与系统性淀粉样变性相关的致命性胰腺炎。
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J Assoc Physicians India. 2000 Nov;48(11):1109-10.
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10
Recurrent AA amyloidosis in a kidney transplant.肾移植后复发性 AA 淀粉样变性。
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本文引用的文献

1
Acquired factor X deficiency in light-chain (AL) amyloidosis is rare and associated with advanced disease.轻链(AL)淀粉样变性中获得性因子X缺乏症罕见,且与晚期疾病相关。
Hematol Oncol Stem Cell Ther. 2019 Mar;12(1):10-14. doi: 10.1016/j.hemonc.2018.05.002. Epub 2018 Jun 28.
2
Al amyloidosis.淀粉样变。
Orphanet J Rare Dis. 2012 Aug 21;7:54. doi: 10.1186/1750-1172-7-54.
3
Long-term survival (10 years or more) in 30 patients with primary amyloidosis.
Blood. 1999 Feb 1;93(3):1062-6.