Department of Neuroendovascular Therapy, St. Luke's International Hospital, Tokyo, Japan.
Department of Neurosurgery, St. Luke's International Hospital, Tokyo, Japan.
Interv Neuroradiol. 2021 Jun;27(3):451-455. doi: 10.1177/1591019920968363. Epub 2020 Oct 22.
A filum terminale arteriovenous fistula (FTAVF) is an extremely rare spinal arteriovenous fistula (AVF) and typically presents with myelopathy and conus medullaris syndrome caused by venous congestion in the spinal cord. Most reported FTAVFs are intradural pial AVFs with perimedullary drainage in the filum terminale interna. However, there are no reports of AVFs in the filum terminale externa (FTE). We describe a case involving a 68-year-old man with an AVF in the FTE who presented with progressive myelopathy and underwent successful endovascular treatment. We identified the specific shunt point by fusing postoperative computed tomography and magnetic resonance images. The features of the extradural sac AVF developed in the FTE may mimic those of a dural AVF with dural supply to the FTE covered by the dural component, unlike typical FTAVFs where the shunt develops at the pia mater. This case makes a significant contribution to the field by increasing the understanding of the clinical characteristics of an AVF that develops in the FTE and its angioarchitecture.
终丝动静脉瘘(FTAVF)是一种极其罕见的脊髓动静脉瘘(AVF),通常表现为因脊髓静脉淤血引起的脊髓病和圆锥综合征。大多数报道的 FTAVF 是终丝内硬脊膜动静脉瘘,伴有终丝内的髓周引流。然而,尚无终丝外(FTE)AVF 的报道。我们描述了一例 68 岁男性 FTE 中的 AVF 病例,该患者表现为进行性脊髓病,并接受了成功的血管内治疗。我们通过融合术后 CT 和磁共振图像来确定特定的分流点。FTE 中发生的硬脊膜外囊动静脉瘘的特征可能与硬脊膜供应 FTE 的硬脊膜成分相似,不同于典型的 FTAVF,其分流发生在软脊膜上。该病例通过增加对 FTE 中发生的 AVF 的临床特征及其血管解剖结构的理解,为该领域做出了重要贡献。