Texas Tech University Health Sciences Center, Lubbock, Texas USA.
Texas Tech University Health Sciences Center, Lubbock, Texas USA.
Am J Med Sci. 2021 Mar;361(3):375-382. doi: 10.1016/j.amjms.2020.09.003. Epub 2020 Sep 3.
In this case report of a patient with angioimmunoblastic T-cell lymphoma (AITL), we describe the occurrence of three sequential complications that have been reported uncommonly in this disease subtype. Firstly, the patient developed hypercalcemia due to elevated 1,25-didydroxyvitamin D. Although hypercalcemia in AITL is not rare (1-2% incidence), this case was unusual in that the complication developed when disease appeared stable and symptomatically, he was doing well otherwise. Hypercalcemia surprisingly resolved a few months later at a time when his disease appeared to be progressing. A year later, the patient presented with digital ischemia necessitating partial amputation of a finger. Pathological exam revealed granulomatous vasculitis of small and medium arterioles with infiltrating malignant T lymphocytes. Although skin manifestations are common in AITL, necrotizing granulomatous vasculitis with accompanying tumor cells leading to severe digital ischemia appears rare. Subsequently the patient developed profound pancytopenia with bone marrow confirming severe aplastic anemia. To our knowledge only one other case of aplastic anemia has been reported in a patient with AITL. We discuss the diagnostic and management considerations involved in this patient care and review similar reported cases.
在这份关于血管免疫母细胞性 T 细胞淋巴瘤(AITL)患者的病例报告中,我们描述了三种连续并发症的发生,这些并发症在这种疾病亚型中很少报道。首先,患者因 1,25-二羟维生素 D 升高而发生高钙血症。虽然 AITL 中的高钙血症并不罕见(发病率为 1-2%),但这种情况很不寻常,因为当疾病表现稳定且症状明显时,并发症发生了,而其他方面他的情况良好。几个月后,高钙血症出人意料地得到了缓解,此时他的疾病似乎正在进展。一年后,患者出现手指缺血性症状,需要部分截肢。病理检查显示小动脉和中等动脉的肉芽肿性血管炎,浸润恶性 T 淋巴细胞。尽管 AITL 常见皮肤表现,但伴有肿瘤细胞导致严重手指缺血的坏死性肉芽肿性血管炎似乎很少见。随后,患者出现严重全血细胞减少,骨髓证实严重再生障碍性贫血。据我们所知,AITL 患者中只有一例再生障碍性贫血的报道。我们讨论了该患者治疗中涉及的诊断和管理注意事项,并回顾了类似的报道病例。