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阻塞性睡眠呼吸暂停综合征伴可逆性肺动脉高压和右心衰竭的诊断难题:病例报告。

Diagnostic dilemma in a case of obstructive sleep apnoea syndrome with reversible pulmonary hypertension and right heart failure: A case report.

机构信息

Department of Pediatrics, Hokkaido University Hospital, Sapporo, Japan; Department of Pediatrics, Japanese Red Cross Kitami Hospital, Kitami, Japan.

Department of Pediatrics, Hokkaido University Hospital, Sapporo, Japan.

出版信息

Int J Pediatr Otorhinolaryngol. 2020 Nov;138:110378. doi: 10.1016/j.ijporl.2020.110378. Epub 2020 Sep 11.

DOI:10.1016/j.ijporl.2020.110378
PMID:33152969
Abstract

Childhood obstructive sleep apnoea syndrome (OSAS) secondary to adenoid hyperplasia is known to give rise to pulmonary hypertension. However, we present a case of a toddler with pulmonary hypertension (PH) and right heart failure due to OSAS, the cause of which is difficult to identify. After the patient underwent an adenotonsillectomy, OSAS disappeared and the PH eventually resolved. Both paediatricians and otolaryngologists should know that paediatric OSAS can occur even in the setting of mild, clinically insignificant palatine tonsil hypertrophy and adenoid hyperplasia. Surgical intervention should be considered without losing the opportunity if it could be the cause of PH.

摘要

儿童阻塞性睡眠呼吸暂停综合征(OSAS)继发于腺样体增生已知可导致肺动脉高压。然而,我们报告了一例因 OSAS 导致肺动脉高压(PH)和右心衰竭的幼儿病例,其病因难以确定。患者行腺样体扁桃体切除术(adenotonsillectomy)后,OSAS 消失,PH 最终得到缓解。儿科医生和耳鼻喉科医生都应该知道,即使在腭扁桃体轻度、临床上无明显增生和腺样体增生的情况下,儿童 OSAS 也可能发生。如果 PH 的病因是 OSAS,应不失时机地考虑手术干预。

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