IgG4 相关硬化性胆管炎——一种巨大的模仿者。
IgG4-related sclerosing cholangitis- A great mimicker.
机构信息
Department of Gastroenterology, All India Institute of Medical Sciences, Bhubaneswar 751 019, India.
出版信息
Indian J Gastroenterol. 2020 Dec;39(6):614-618. doi: 10.1007/s12664-020-01102-2. Epub 2020 Nov 6.
IgG4-related disease (IgG4 RD) is a multisystem disorder characterized by tumefactive (mass forming) lesions, storiform fibrosis, and IgG4-positive plasma cell infiltration. IgG4 sclerosing cholangitis (IgG4 SC) is the biliary manifestation of IgG4 RD, often in association with autoimmune pancreatitis (AIP). Here, we report two patients with IgG4-related cholangitis mimicking primary sclerosing cholangitis.
IgG4 相关疾病（IgG4 RD）是一种多系统疾病，其特征是肿块样（形成肿块）病变、席纹状纤维化和 IgG4 阳性浆细胞浸润。IgG4 硬化性胆管炎（IgG4 SC）是 IgG4 RD 的胆管表现，常与自身免疫性胰腺炎（AIP）相关。在此，我们报告了两例 IgG4 相关胆管炎模仿原发性硬化性胆管炎的病例。
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