Valiyeva Sayali, Romano Lucia, Schietroma Mario, Carlei Francesco, Giuliani Antonio
Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, Department of Surgery, San Salvatore Hospital, Italy.
Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, Department of Surgery, San Salvatore Hospital, Italy.
Int J Surg Case Rep. 2020;77S(Suppl):S17-S20. doi: 10.1016/j.ijscr.2020.10.029. Epub 2020 Oct 10.
Agenesis of the dorsal pancreas (ADP) is a rare congenital anomaly resulting in missing corpus and cauda of the pancreas. The possibility of finding this disorder is increasing with the use of advanced radiological techniques like CT scan or MRI.
We reported 2 cases of a partial ADP as radiological finding: the first one was a 79-year-old asymptomatic patient who presented to perform a CT staging scan for bladder tumor, while the second case was a 73-year-old patient with obstructive jaundice and with suspected common bile duct calculi. In the second patient US, CT scan and MRI were performed, and after that also an ERCP was scheduled.
The prevalence of agenesis of the dorsal pancreas is not exactly known; in the literature, only 50 cases have been reported. Its cause and pathogenesis are not fully understood. Some patients experience no symptoms, while others may develop hyperglycemia, diabetes mellitus, bile duct obstruction, abdominal pain, pancreatitis, or other conditions.
Considering that dorsal agenesis is sporadically found, often do not have related symptoms and it does not require a specific treatment, whether further examinations are needed to determine the type of agenesis remains questioned.
背侧胰腺发育不全（ADP）是一种罕见的先天性异常，导致胰腺体部和尾部缺失。随着CT扫描或MRI等先进放射技术的应用，发现这种疾病的可能性正在增加。
我们报告了2例作为放射学表现的部分ADP病例：第一例是一名79岁无症状患者，因膀胱肿瘤进行CT分期扫描；第二例是一名73岁患有梗阻性黄疸且怀疑有胆总管结石的患者。对第二例患者进行了超声、CT扫描和MRI检查，之后还安排了内镜逆行胰胆管造影（ERCP）。
背侧胰腺发育不全的患病率尚不完全清楚；文献中仅报道了50例。其病因和发病机制尚未完全了解。一些患者没有症状，而另一些患者可能会出现高血糖、糖尿病、胆管梗阻、腹痛、胰腺炎或其他病症。
鉴于背侧发育不全是偶尔发现的，通常没有相关症状且不需要特殊治疗，是否需要进一步检查以确定发育不全的类型仍存在疑问。
