Ehret M, Jacobi G, Hey A, Segerer S
Neurological Institute, University of Frankfurt, FRG.
Clin Neuropathol. 1987 Sep-Oct;6(5):218-23.
We report on two cases of congenital primitive neuroectodermal tumors located in the posterior cranial fossa. They were symptomatic at birth with occlusive internal hydrocephalus. Clinical investigations had failed to diagnose brain tumors and had led to the suggestion of maldevelopment syndromes. In one of these children a malignant rhabdoid tumor of the kidney was operated at the age of 4 1/2 months. Autopsy revealed medulloblastoma combined with a malignant rhabdoid tumor of the kidney in one case and ependymoblastoma in the other.
我们报告两例位于颅后窝的先天性原始神经外胚层肿瘤。患儿出生时即出现症状，伴有梗阻性内部脑积水。临床检查未能诊断出脑肿瘤，曾怀疑为发育异常综合征。其中一名儿童在4个半月大时接受了肾恶性横纹肌样瘤手术。尸检发现，一例为髓母细胞瘤合并肾恶性横纹肌样瘤，另一例为室管膜母细胞瘤。
