Division of Congenital Cardiovascular Surgery, University Children's Hospital Zurich, Zurich, Switzerland.
Department of Cardiac Surgery, University Heart Center, University Hospital Zurich, Zurich, Switzerland.
Interact Cardiovasc Thorac Surg. 2021 Apr 8;32(3):497-498. doi: 10.1093/icvts/ivaa268.
Atresia of the left main coronary artery is a rare coronary anomaly. We describe the case of a 5-year-old child presenting in emergency in extremis. Clinical findings of haemodynamic collapse, malignant ventricular tachyarrhythmias and severe mitral regurgitation were indicative of a possible ischaemic aetiology. Surgical revascularization of the atretic left main coronary artery segment using an interposition autologous saphenous vein graft was successfully performed.
左主干冠状动脉闭锁是一种罕见的冠状动脉异常。我们描述了一例 5 岁儿童在极端情况下紧急就诊的病例。血流动力学崩溃、恶性室性心律失常和严重二尖瓣反流的临床发现提示可能存在缺血性病因。使用自体大隐静脉移植物对闭锁的左主干冠状动脉段进行了成功的外科血运重建。