Shayesteh Shahab, Salimian Kevan J, Fouladi Daniel Fadaei, Blanco Alejandra, Fishman Elliot K, Kawamoto Satomi
The Russell H. Morgan Department of Radiology and Radiological Science, Johns Hopkins University School of Medicine, JHOC 3140E, 601 North Caroline St, Baltimore, MD, USA.
Department of Pathology, Johns Hopkins University School of Medicine, JHOC 3140E, 601 North Caroline St, Baltimore, MD, USA.
Radiol Case Rep. 2020 Nov 11;16(1):123-127. doi: 10.1016/j.radcr.2020.10.052. eCollection 2021 Jan.
Lymphangioma is a rare, benign congenital malformation of the lymphatic system that usually affects the neck and head in children. Intra-abdominal lymphangioma accounts for less than 5 percent of all cases of lymphangioma. The clinical presentation of intra-abdominal lymphangioma can vary from asymptomatic to nausea, vomiting, and abdominal pain. The diagnosis of intra-abdominal lymphangioma is based on imaging modalities and histopathological examination. The definitive treatment is surgical resection. Here we describe the interesting and rare case of a 29-year-old woman with lymphangioma of the retroperitoneum extending to the root of the mesentery. We focus on the diagnosis and management of this rare tumor by the application of radiological modalities and pathological analysis.
淋巴管瘤是一种罕见的良性先天性淋巴系统畸形，通常影响儿童的颈部和头部。腹腔内淋巴管瘤占所有淋巴管瘤病例的不到5%。腹腔内淋巴管瘤的临床表现可从无症状到恶心、呕吐和腹痛不等。腹腔内淋巴管瘤的诊断基于影像学检查和组织病理学检查。 definitive treatment是手术切除。在此，我们描述了一例29岁女性患有腹膜后淋巴管瘤并延伸至肠系膜根部的有趣且罕见的病例。我们通过应用放射学检查方法和病理分析来关注这种罕见肿瘤的诊断和治疗。
