Hu Jian, Zhao Xiaoyun, Wu Qian, Liu Beibei, Chen Chi, Bian Panpan, Guo Yufen, Xu Baicheng
Department of Otorhinolaryngology Head and Neck Surgery,the Second Hospital of Lanzhou University,Lanzhou,730030,China.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2020 Nov;34(11):981-986. doi: 10.13201/j.issn.2096-7993.2020.11.005.
To investigate the distribution of common inner ear and internal auditory canal malformations in children with single-sided deafness(SSD) ,and to explore the imaging etiology of SSD by comparing the quantitative parameters of key bone structures between deaf and normal ears in children with congenital SSD. Forty children with SSD diagnosed in the Second Hospital of Lanzhou University from September 2016 to March 2019 were collected. All of them underwent HRCT examinations of temporal bone . The area of bone island, the width of vestibular, the width of internal auditory canal, the height of cochlear and the width of cochlear basal axis were measured. Paired t test was used to compare the difference between the hearing abnormality and normal hearing in children with SSD. The rate of inner ear deformity was 62.5% in SSD group,the most common deformity was cochlear nerve canal deformity, 20 cases (50.0%) of cochlear canal stenosis and 3 cases (7.5%) of cochlear canal atresia.The second most common deformity was internal auditory canal deformity, including 5 cases (12.5%) of internal auditory canal stenosis and 1 case (2.5%) of internal auditory canal atresia. Other malformations included 1 case(2.5%) of RO, 2 cases (5.0%) of incomplete partition (IP) type II and 1 case (2.5%) of enlargement of vestibular aqueduct (EVA). There are no significant difference in the measured results of the key structures of the inner ear between two groups except the width of cochlear nerve canal, internal auditory canal and the area of bone island. The main inner ear deformities in children with SSD are cochlear nerve canal stenosis and inner auditory canal stenosis. HRCT of temporal bone has high diagnostic value for inner ear deformities in children with SSD.
探讨单侧耳聋(SSD)患儿常见内耳及内耳道畸形的分布情况,并通过比较先天性SSD患儿患侧与健侧耳关键骨结构的定量参数,探索SSD的影像学病因。收集2016年9月至2019年3月在兰州大学第二医院确诊的40例SSD患儿。所有患儿均接受颞骨高分辨率CT(HRCT)检查。测量骨岛面积、前庭宽度、内耳道宽度、耳蜗高度及耳蜗基底轴宽度。采用配对t检验比较SSD患儿听力异常与听力正常者之间的差异。SSD组内耳畸形率为62.5%,最常见的畸形为蜗神经管畸形,蜗神经管狭窄20例(50.0%),蜗神经管闭锁3例(7.5%)。第二常见的畸形为内耳道畸形,包括内耳道狭窄5例(12.5%),内耳道闭锁1例(2.5%)。其他畸形包括1例(2.5%)半规管畸形、2例(5.0%)II型不完全分隔(IP)及1例(2.5%)前庭导水管扩大(EVA)。除蜗神经管宽度、内耳道宽度及骨岛面积外,两组内耳关键结构测量结果差异无统计学意义。SSD患儿主要内耳畸形为蜗神经管狭窄及内耳道狭窄。颞骨HRCT对SSD患儿内耳畸形具有较高的诊断价值。