Suppr超能文献

无肌病性皮肌炎合并周围神经病。

Amyopathic dermatomyositis combined with peripheral neuropathy.

机构信息

Neurology, University of Tsukuba Hospital, Tsukuba, Ibaraki, Japan.

Neurology, University of Tsukuba Hospital, Tsukuba, Ibaraki, Japan

出版信息

BMJ Case Rep. 2020 Nov 30;13(11):e237250. doi: 10.1136/bcr-2020-237250.

Abstract

We provide the first report of amyopathic dermatomyositis combined with peripheral neuropathy. Our patient, a 49-year-old woman, initially experienced muscle weakness and tingling sensations in her legs, and nerve conduction study findings and the detection of antiganglioside antibodies indicated that she had autoimmune peripheral neuropathy. The unexpected presence of skin lesions, interstitial pneumonia and antibodies to melanoma differentiation-associated protein 5 prompted an additional diagnosis of amyopathic dermatomyositis. No previous report has described amyopathic dermatomyositis with peripheral neuropathy, and the present case provides evidence for the once-controversial concept of neuromyositis.

摘要

我们提供了首例无肌病性皮肌炎合并周围神经病的报告。我们的患者为一名 49 岁女性,最初出现腿部肌肉无力和刺痛感,神经传导研究结果和抗神经节苷脂抗体检测表明她患有自身免疫性周围神经病。意外出现的皮肤病变、间质性肺炎和黑色素瘤分化相关蛋白 5 抗体促使进一步诊断为无肌病性皮肌炎。之前没有报告描述过无肌病性皮肌炎伴周围神经病,本病例为一度存在争议的神经肌炎概念提供了证据。

相似文献

1
Amyopathic dermatomyositis combined with peripheral neuropathy.
BMJ Case Rep. 2020 Nov 30;13(11):e237250. doi: 10.1136/bcr-2020-237250.
2
Amyopathic dermatomyositis complicated with eosinophilic pneumonia.
Intern Med. 2014;53(14):1539-44. doi: 10.2169/internalmedicine.53.0738. Epub 2014 Jul 15.
3
Amyopathic Dermatomyositis Associated with Histopathological Findings of Organizing Pneumonia and Pulmonary Vasculitis.
Balkan Med J. 2017 Aug 4;34(4):374-377. doi: 10.4274/balkanmedj.2016.1061. Epub 2017 Apr 13.
4
Amyopathic dermatomyositis or dermatomyositis-like skin disease: retrospective review of 16 cases with amyopathic dermatomyositis.
Clin Rheumatol. 2009 Aug;28(8):979-84. doi: 10.1007/s10067-009-1152-9. Epub 2009 Mar 18.
6
Interstitial lung disease in amyopathic dermatomyositis, dermatomyositis and polymyositis.
Eur Respir J. 2003 Aug;22(2):245-50. doi: 10.1183/09031936.03.00026703.
7
Amyopathic dermatomyositis.
Curr Rheumatol Rep. 2001 Aug;3(4):346-51. doi: 10.1007/s11926-001-0039-9.

引用本文的文献

本文引用的文献

1
The diagnosis and classification of amyopathic dermatomyositis: a historical review and assessment of existing criteria.
Br J Dermatol. 2019 May;180(5):1001-1008. doi: 10.1111/bjd.17536. Epub 2019 Feb 25.
3
Amyopathic Dermatomyositis: A Concise Review of Clinical Manifestations and Associated Malignancies.
Am J Clin Dermatol. 2016 Oct;17(5):509-518. doi: 10.1007/s40257-016-0199-z.
4
Dermatomyositis-associated sensory neuropathy: a unifying pathogenic hypothesis.
J Clin Neuromuscul Dis. 2014 Sep;16(1):7-11. doi: 10.1097/CND.0000000000000048.
7
Adult dermatomyositis with severe polyneuropathy: does neuromyositis exist?
Neurol Sci. 2010 Jun;31(3):373-6. doi: 10.1007/s10072-010-0246-0. Epub 2010 Mar 13.
8
Activation of melanoma differentiation-associated gene 5 causes rapid involution of the thymus.
J Immunol. 2009 May 15;182(10):6044-50. doi: 10.4049/jimmunol.0803809.
9
Serum VEGF levels in POEMS syndrome and in immune-mediated neuropathies.
Neurology. 2009 Mar 17;72(11):1024-6. doi: 10.1212/01.wnl.0000344569.13496.ff.

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验