• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

主谋:一个用于实证证据整理和基因变异解读的综合基因组关联搜索引擎。

Mastermind: A Comprehensive Genomic Association Search Engine for Empirical Evidence Curation and Genetic Variant Interpretation.

作者信息

Chunn Lauren M, Nefcy Diane C, Scouten Rachel W, Tarpey Ryan P, Chauhan Gurinder, Lim Megan S, Elenitoba-Johnson Kojo S J, Schwartz Steven A, Kiel Mark J

机构信息

Genomenon Inc., Ann Arbor, MI, United States.

The Johns Hopkins Hospital, Department of Pharmacy, Baltimore, MD, United States.

出版信息

Front Genet. 2020 Nov 13;11:577152. doi: 10.3389/fgene.2020.577152. eCollection 2020.

DOI:10.3389/fgene.2020.577152
PMID:33281875
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7691534/
Abstract

Design and interpretation of genome sequencing assays in clinical diagnostics and research labs is complicated by an inability to identify information from the medical literature and related databases quickly, comprehensively and reproducibly. This challenge is compounded by the complexity and heterogeneity of nomenclatures used to describe diseases, genes and genetic variants. Mastermind is a widely-used bioinformatic platform of genomic associations that has indexed more than 7.5 M full-text articles and 2.5 M supplemental datasets. It has automatically identified, disambiguated and annotated >6.1 M genetic variants and identified >50 K disease-gene associations. Here, we describe how Mastermind improves the sensitivity and reproducibility of clinical variant interpretation and produces comprehensive genomic landscapes of genetic variants driving pharmaceutical research. We demonstrate an alarmingly high degree of heterogeneity across commercially available panels for hereditary cancer that is resolved by evidence from Mastermind. We further examined the sensitivity of Mastermind for variant interpretation by examining 108 clinically-encountered variants and comparing the results to alternate methods. Mastermind demonstrated a sensitivity of 98.4% compared to 4.4, 45.6, and 37.4% for alternatives PubMed, Google Scholar, and ClinVar, respectively, and a specificity of 98.5% compared to 45.1, 57.6, and 68.8% as well as an increase in content yield of 22.6-, 2.2-, and 2.6-fold. When curated for clinical significance, Mastermind identified more than 4.9-fold more pathogenic variants than ClinVar for representative genes. For structural variants, we compared Mastermind's ability to sensitively identify evidence for 10 representative disease-causing CNVs versus results identified in PubMed, as well as its ability to identify evidence for fusion events compared to COSMIC. Mastermind demonstrated a 4.0- to 43.9-fold increase in references for specific CNVs compared to PubMed, as well as 5.4-fold more fusion genes when compared with COSMIC's curated database. Additionally, Mastermind produced an 8.0-fold increase in reference citations for fusion events common to Mastermind and outside databases. Taken together, these results demonstrate the utility and superiority of Mastermind in terms of both sensitivity and specificity of automated results for clinical diagnostic variant interpretation for multiple genetic variant types and highlight the potential benefit in informing pharmaceutical research.

摘要

在临床诊断和研究实验室中,由于无法快速、全面且可重复地从医学文献和相关数据库中识别信息,基因组测序检测的设计和解读变得复杂。用于描述疾病、基因和基因变异的命名法的复杂性和异质性,使这一挑战更加严峻。Mastermind是一个广泛使用的基因组关联生物信息平台,已索引超过750万篇全文文章和250万个补充数据集。它已自动识别、消除歧义并注释了超过610万个基因变异,并识别出超过5万个疾病-基因关联。在这里,我们描述了Mastermind如何提高临床变异解读的敏感性和可重复性,并生成推动药物研究的基因变异的全面基因组图谱。我们展示了市售遗传性癌症检测板之间存在惊人的高度异质性,而Mastermind的证据解决了这一问题。我们通过检查108个临床遇到的变异,并将结果与其他方法进行比较,进一步研究了Mastermind对变异解读的敏感性。与替代方法PubMed、Google Scholar和ClinVar相比,Mastermind的敏感性分别为98.4%,而替代方法的敏感性分别为4.4%、45.6%和37.4%;特异性分别为98.5%,而替代方法的特异性分别为45.1%、57.6%和68.8%,内容产量分别提高了22.6倍、2.2倍和2.6倍。当针对临床意义进行整理时,Mastermind识别出的代表性基因的致病变异比ClinVar多4.9倍以上。对于结构变异,我们比较了Mastermind敏感识别1十条代表性致病CNV证据的能力与PubMed中识别的结果,以及与COSMIC相比其识别融合事件证据的能力。与PubMed相比,Mastermind展示了特定CNV的参考文献增加了4倍至4一3.9倍,与COSMIC的整理数据库相比,融合基因增加了5.4倍。此外,Mastermind对于Mastermind和外部数据库共有的融合事件,参考文献引用增加了8.0倍。综上所述,这些结果证明了Mastermind在多种基因变异类型的临床诊断变异解读自动结果的敏感性和特异性方面的实用性和优越性,并突出了其在为药物研究提供信息方面的潜在益处。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/63a0df44af71/fgene-11-577152-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/4293a4a6f314/fgene-11-577152-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/7b02e234f744/fgene-11-577152-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/63a0df44af71/fgene-11-577152-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/4293a4a6f314/fgene-11-577152-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/7b02e234f744/fgene-11-577152-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/be2c/7691534/63a0df44af71/fgene-11-577152-g003.jpg

相似文献

1
Mastermind: A Comprehensive Genomic Association Search Engine for Empirical Evidence Curation and Genetic Variant Interpretation.主谋:一个用于实证证据整理和基因变异解读的综合基因组关联搜索引擎。
Front Genet. 2020 Nov 13;11:577152. doi: 10.3389/fgene.2020.577152. eCollection 2020.
2
Evaluation of literature searching tools for curation of mismatch repair gene variants in hereditary colon cancer.用于遗传性结肠癌错配修复基因变异整理的文献检索工具评估
Adv Genet (Hoboken). 2021 Feb 18;2(1):e10039. doi: 10.1002/ggn2.10039. eCollection 2021 Mar.
3
Folic acid supplementation and malaria susceptibility and severity among people taking antifolate antimalarial drugs in endemic areas.在流行地区,服用抗叶酸抗疟药物的人群中,叶酸补充剂与疟疾易感性和严重程度的关系。
Cochrane Database Syst Rev. 2022 Feb 1;2(2022):CD014217. doi: 10.1002/14651858.CD014217.
4
AVADA: toward automated pathogenic variant evidence retrieval directly from the full-text literature.AVADA:从全文文献中直接进行自动化的致病性变异证据检索。
Genet Med. 2020 Feb;22(2):362-370. doi: 10.1038/s41436-019-0643-6. Epub 2019 Aug 30.
5
Genome analysis and knowledge-driven variant interpretation with TGex.基因组分析和基于 TGex 的知识驱动的变异解释。
BMC Med Genomics. 2019 Dec 30;12(1):200. doi: 10.1186/s12920-019-0647-8.
6
Copy number variant discrepancy resolution using the ClinGen dosage sensitivity map results in updated clinical interpretations in ClinVar.使用 ClinGen 剂量敏感性图谱的拷贝数变异差异解决方法可在 ClinVar 中更新临床解释。
Hum Mutat. 2018 Nov;39(11):1650-1659. doi: 10.1002/humu.23610.
7
MAGPEL: an autoMated pipeline for inferring vAriant-driven Gene PanEls from the full-length biomedical literature.MAGPEL:从全文献中自动推断变异驱动的基因面板的自动化管道。
Sci Rep. 2020 Jul 23;10(1):12365. doi: 10.1038/s41598-020-68649-0.
8
Assessment of an automated approach for variant interpretation in screening for monogenic disorders: A single-center study.单中心研究评估一种用于单基因疾病筛查中变异解读的自动化方法。
Mol Genet Genomic Med. 2022 Dec;10(12):e2085. doi: 10.1002/mgg3.2085. Epub 2022 Nov 5.
9
Identification of germline population variants misclassified as cancer-associated somatic variants.识别被误分类为癌症相关体细胞变异的种系群体变异。
Front Med (Lausanne). 2024 Mar 20;11:1361317. doi: 10.3389/fmed.2024.1361317. eCollection 2024.
10
ClinGen Variant Curation Expert Panel experiences and standardized processes for disease and gene-level specification of the ACMG/AMP guidelines for sequence variant interpretation.ClinGen 变异体管理专家小组在疾病和基因水平上规范 ACMG/AMP 序列变异解释指南的经验和标准化流程。
Hum Mutat. 2018 Nov;39(11):1614-1622. doi: 10.1002/humu.23645.

引用本文的文献

1
Geno4ME Study: implementation of whole genome sequencing for population screening in a large healthcare system.Geno4ME研究:在大型医疗保健系统中实施全基因组测序用于人群筛查。
NPJ Genom Med. 2025 Jul 1;10(1):50. doi: 10.1038/s41525-025-00508-1.
2
An ABCB11 variant registry and novel knockin mouse model of PFIC2 based on the clinically relevant ABCB11 E297G variant.基于临床相关的ABCB11 E297G变体的ABCB11变体登记库和PFIC2新型敲入小鼠模型。
J Lipid Res. 2025 Jul;66(7):100840. doi: 10.1016/j.jlr.2025.100840. Epub 2025 Jun 11.
3
The ALPL gene variant project: results of the first 100 reclassified variants.

本文引用的文献

1
AVADA: toward automated pathogenic variant evidence retrieval directly from the full-text literature.AVADA:从全文文献中直接进行自动化的致病性变异证据检索。
Genet Med. 2020 Feb;22(2):362-370. doi: 10.1038/s41436-019-0643-6. Epub 2019 Aug 30.
2
The Genomic Landscape of Mucinous Breast Cancer.黏液性乳腺癌的基因组特征
J Natl Cancer Inst. 2019 Jul 1;111(7):737-741. doi: 10.1093/jnci/djy216.
3
PAX5-driven subtypes of B-progenitor acute lymphoblastic leukemia.PAX5 驱动的 B 系前体细胞急性淋巴细胞白血病亚型。
碱性磷酸酶基因变异项目:前100个重新分类变异的结果
JBMR Plus. 2025 Mar 17;9(6):ziaf044. doi: 10.1093/jbmrpl/ziaf044. eCollection 2025 Jun.
4
Clinical utility of panel-based genetic sequencing for von Willebrand disease.基于基因panel测序在血管性血友病诊断中的临床应用
Res Pract Thromb Haemost. 2025 Mar 12;9(2):102730. doi: 10.1016/j.rpth.2025.102730. eCollection 2025 Feb.
5
Accelerating genetic diagnostics in retinitis pigmentosa: implementation of a semi-automated bespoke cohort analysis workflow for Hong Kong Genome Project.加速色素性视网膜炎的基因诊断:为香港基因组计划实施半自动定制队列分析工作流程
Hum Genet. 2025 May;144(5):515-528. doi: 10.1007/s00439-025-02737-x. Epub 2025 Mar 31.
6
Pathogenic variants in the Alport genes are prevalent in the Singapore multiethnic population with highest frequency in the Chinese.奥尔波特基因的致病性变异在新加坡多民族人群中普遍存在,其中华人的频率最高。
Sci Rep. 2025 Mar 5;15(1):7691. doi: 10.1038/s41598-025-92520-9.
7
Genetic Landscape of Dystonia in Asian Indians.亚洲印度人肌张力障碍的遗传图谱
Mov Disord Clin Pract. 2025 May;12(5):594-601. doi: 10.1002/mdc3.14325. Epub 2025 Jan 3.
8
Prequalification of genome-based newborn screening for severe childhood genetic diseases through federated training based on purifying hyperselection.通过基于纯化超选择的联合训练对严重儿童遗传病进行基于基因组的新生儿筛查预认证。
Am J Hum Genet. 2024 Dec 5;111(12):2618-2642. doi: 10.1016/j.ajhg.2024.10.021.
9
Genomic profiling and expanded use of targeted anticancer drugs in solid cancers with exhausted evidence-based treatment options (PRECODE): study protocol of a prospective, non-randomized, cohort study.基因组分析和针对已穷尽循证治疗选择的实体瘤中靶向抗癌药物的扩展应用(PRECODE):一项前瞻性、非随机、队列研究的研究方案。
BMC Med Genomics. 2024 Nov 21;17(1):274. doi: 10.1186/s12920-024-02033-z.
10
An estimation of global genetic prevalence of PLA2G6-associated neurodegeneration.PLA2G6 相关神经退行性疾病的全球遗传患病率估计。
Orphanet J Rare Dis. 2024 Oct 18;19(1):388. doi: 10.1186/s13023-024-03275-x.
Nat Genet. 2019 Feb;51(2):296-307. doi: 10.1038/s41588-018-0315-5. Epub 2019 Jan 14.
4
COSMIC: the Catalogue Of Somatic Mutations In Cancer.COSMIC:癌症体细胞突变目录。
Nucleic Acids Res. 2019 Jan 8;47(D1):D941-D947. doi: 10.1093/nar/gky1015.
5
BRAF fusions identified in melanomas have variable treatment responses and phenotypes.在黑色素瘤中鉴定出的 BRAF 融合具有不同的治疗反应和表型。
Oncogene. 2019 Feb;38(8):1296-1308. doi: 10.1038/s41388-018-0514-7. Epub 2018 Sep 25.
6
Novel KHDRBS1-NTRK3 rearrangement in a congenital pediatric CD34-positive skin tumor: a case report.先天性小儿 CD34 阳性皮肤肿瘤中新型 KHDRBS1-NTRK3 重排:病例报告。
Virchows Arch. 2019 Jan;474(1):111-115. doi: 10.1007/s00428-018-2415-0. Epub 2018 Sep 6.
7
Driver Fusions and Their Implications in the Development and Treatment of Human Cancers.驱动融合及其在人类癌症发生和治疗中的意义。
Cell Rep. 2018 Apr 3;23(1):227-238.e3. doi: 10.1016/j.celrep.2018.03.050.
8
ClinVar: improving access to variant interpretations and supporting evidence.ClinVar:改善变异解读和支持证据的获取。
Nucleic Acids Res. 2018 Jan 4;46(D1):D1062-D1067. doi: 10.1093/nar/gkx1153.
9
Mutational landscape of metastatic cancer revealed from prospective clinical sequencing of 10,000 patients.从10000例患者的前瞻性临床测序中揭示的转移性癌症的突变图谱。
Nat Med. 2017 Jun;23(6):703-713. doi: 10.1038/nm.4333. Epub 2017 May 8.
10
Clinical Variant Classification: A Comparison of Public Databases and a Commercial Testing Laboratory.临床变异分类:公共数据库与商业检测实验室的比较
Oncologist. 2017 Jul;22(7):797-803. doi: 10.1634/theoncologist.2016-0431. Epub 2017 Apr 13.