Department of Surgery. University Hospital Centre Zagreb, Zagreb, Croatia.
Department of Gastroenterology. University Hospital Centre Zagreb, Zagreb, Croatia.
Cir Cir. 2020;88(Suppl 2):66-70. doi: 10.24875/CIRU.20000342.
We report a case of ruptured liver hematoma as a result of suppurated arteriovenous malformation (AVM) in a patient with Rendu-Osler-Weber (ROW) syndrome. The patient presented with unexplained fever and upper right abdominal pain associated with microcytic anemia. A computed tomography scan revealed increasing subcapsular liver hematoma and features of liver abscess. Intraoperatively, a left liver hematoma mixed with pus was found that was attached to the anterior abdominal wall. Surgery included left lateral bisegmentectomy, while pathohistological analysis showed AVM and genetic tests confirmed ROW. This is the first such life-threatening surgical case of ROW complication reported in the scientific literature.
我们报告了一例因并发化脓性动静脉畸形（AVM）而导致肝血肿破裂的 Rendu-Osler-Weber（ROW）综合征患者。该患者出现不明原因的发热和右上腹痛，同时伴有小细胞性贫血。计算机断层扫描显示肝包膜下血肿增大，并有肝脓肿的特征。术中发现左肝血肿混合脓液，与前腹壁粘连。手术包括左外侧半肝切除术，而组织病理学分析显示 AVM，基因检测证实为 ROW。这是科学文献中首例报道的 ROW 并发症导致如此危及生命的手术案例。
