1例洛伊斯-迪茨综合征患者主动脉根部假性动脉瘤的经动脉弹簧圈栓塞术：病例报告
Transarterial coil embolization of an aortic root pseudoaneurym in a patient with Loeys-Dietz syndrome: a case report.
作者信息
D'Ortenzio Robert, Cardarelli-Leite Leandro, Dhatt Ravjot, Saw Jacqueline, Heran Manraj
机构信息
Department of Radiology, University of British Columbia, 11th Floor, 2775 Laurel St., Vancouver, V5Z 1M9, Canada.
Department of Radiology, Western University, 1151 Richmond St, London, N6A 3K7, Canada.
出版信息
CVIR Endovasc. 2020 Dec 8;3(1):94. doi: 10.1186/s42155-020-00184-5.
BACKGROUND
Loeys-Dietz syndrome (LDS) is a rare autosomal-dominant connective tissue disorder characterized by arterial aneurysms and vascular friability. Surgical intervention for LDS patients carries significant morbidity and mortality. Currently, the standard management of aortic root pseudoaneurysms is surgical intervention.
CASE PRESENTATION
A 20 year old male with LDS presented with a progressively enlarging ascending aortic aneurysm. He underwent a Bentall-type aortic root replacement complicated by a 20 mm aortic root anastomotic pseudoaneurysm. Due to the patient's high risk for repeat surgical intervention, he underwent successful transarterial coil embolization of his aortic root pseudoaneurysm without complication.
CONCLUSIONS
Coil embolization may provide an alternative treatment for patients presenting with aortic root pseudoaneurysm who are high risk for traditional surgical treatment, such as those with connective tissue disease.
背景
洛伊斯-迪茨综合征（LDS）是一种罕见的常染色体显性遗传性结缔组织疾病，其特征为动脉动脉瘤和血管脆性增加。LDS患者的手术干预具有显著的发病率和死亡率。目前，主动脉根部假性动脉瘤的标准治疗方法是手术干预。
病例介绍
一名20岁的LDS男性患者出现升主动脉瘤逐渐增大。他接受了Bentall型主动脉根部置换术，但术后出现了一个20毫米的主动脉根部吻合口假性动脉瘤。由于患者再次进行手术干预的风险较高，他成功接受了经动脉线圈栓塞术治疗主动脉根部假性动脉瘤，且未出现并发症。
结论
对于传统手术治疗风险较高的主动脉根部假性动脉瘤患者，如患有结缔组织疾病的患者，线圈栓塞术可能是一种替代治疗方法。
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