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[通过超声检查、X线计算机断层扫描和核磁共振对拉塞尔间脑性恶病质进行诊断及随访]

[Diagnosis and follow-up of Russel's diencephalic cachexia by echography, x-ray computed tomography and nuclear magnetic resonance].

作者信息

Dabadie A, Roussey M, Journel H, Gandon Y, Legall E, Benhasel M, Faivre J

机构信息

Service de pédiatrie-génétique médicale, CHU Pontchaillou, Rennes, France.

出版信息

Pediatrie. 1987;42(9):705-9.

PMID:3330195
Abstract

A diencephalic astrocytoma was diagnosed by ultrasonography in a 5 months old girl with nystagmus and emaciation. A 27 months follow-up with ultrasonography, computed tomography and magnetic resonance imaging, showed an initial improvement after irradiation and afterwards the development of complications with ventricular dilatation and parenchymal calcifications.

摘要

一名5个月大、患有眼球震颤和消瘦的女童经超声检查诊断为间脑星形细胞瘤。通过超声检查、计算机断层扫描和磁共振成像进行了27个月的随访,结果显示放疗后最初有所改善,随后出现了脑室扩张和实质钙化等并发症。

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1
[Diagnosis and follow-up of Russel's diencephalic cachexia by echography, x-ray computed tomography and nuclear magnetic resonance].[通过超声检查、X线计算机断层扫描和核磁共振对拉塞尔间脑性恶病质进行诊断及随访]
Pediatrie. 1987;42(9):705-9.
2
[Diencephalic cachexia (A. Russel's syndrome). Apropos of 3 cases. Importance of transfontanelle ultrasonography].[间脑性恶病质(A. 拉塞尔综合征)。附3例报告。前囟超声检查的重要性]
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[Echographic diagnosis of a cachexia-inducing diencephalic tumor].[引起恶病质的间脑肿瘤的超声诊断]
Arch Fr Pediatr. 1983 Aug-Sep;40(7):575-7.
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[Cachexia caused by a diencephalic tumor in a 3-year-old girl. Physiopathological study and nosological discussion].[一名3岁女童因间脑肿瘤导致恶病质。生理病理学研究与疾病分类学讨论]
Diabete. 1967 Jan-Mar;15(1):57-65.
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[A case report of Russel's diencephalic cachexia].[一例罗素间脑性恶病质病例报告]
Ann Pediatr (Paris). 1992 Mar;39(3):189-93.
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[Diencephalic syndrome. Case report and review of literature].[间脑综合征。病例报告及文献综述]
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Diencephalic syndrome: a rare and easily overlooked cause of failure to thrive.间脑综合征:一种导致发育不良的罕见且易被忽视的病因。
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[Cachectic diencephalic syndrome caused by an anterior hypothalamic tumor. Description of a new case].[下丘脑前部肿瘤所致恶病质性间脑综合征。1例新病例报告]
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[Russel's syndrome: diencephalic tumor in a child].[罗素综合征:儿童间脑肿瘤]
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An oligo astrocytoma with widespread calcification along axonal fibres.一个伴有沿轴突纤维广泛钙化的少突星形细胞瘤。
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