Department of Medicine, Walter Reed National Military Medical Center, Bethesda, Maryland, USA
Department of Medicine, Walter Reed National Military Medical Center, Bethesda, Maryland, USA.
BMJ Case Rep. 2020 Dec 17;13(12):e237560. doi: 10.1136/bcr-2020-237560.
Drug reaction with eosinophilia and systemic symptoms (DRESS) syndrome is a life-threatening condition characterised by peripheral eosinophilia, rash and multi-organ failure arising several weeks after exposure to the culprit medication. Although rare, DRESS syndrome triggered by specific agents has been associated with specific genetic polymorphisms more prevalent in different ethnic groups, including an association between dapsone-induced DRESS and Human Leukocyte Antigen (HLA)-B:13*01, a single nucleotide polymorphism more prevalent in those of Asian descent. DRESS and drug-related vasculitis may affect any organ system including the central nervous system (CNS), usually manifesting as encephalitis, meningitis or embolic cerebrovascular accidents related to eosinophilic cardiac disease and thrombosis. CNS vasculitis is a much rarer complication of drug reactions that may manifest as multifocal ischemia on neuroimaging. In circumstances of drug-related vasculitides, treatment with high-dose corticosteroids may lead to rapid improvement and, ultimately, resolution of associated focal neurologic deficits.
药物反应伴嗜酸性粒细胞增多和全身症状(DRESS)综合征是一种危及生命的疾病,其特征是外周血嗜酸性粒细胞增多、皮疹和多器官衰竭,这些症状在接触致病药物数周后出现。虽然罕见,但某些药物引起的 DRESS 综合征与特定的遗传多态性有关,这些多态性在不同种族中更为常见,包括氨苯砜诱导的 DRESS 与人类白细胞抗原(HLA)-B:13*01 之间的关联,这种单核苷酸多态性在亚洲血统人群中更为常见。DRESS 和药物相关性血管炎可影响包括中枢神经系统(CNS)在内的任何器官系统,通常表现为脑炎、脑膜炎或栓塞性脑血管意外,与嗜酸性心脏病和血栓形成有关。CNS 血管炎是药物反应的一种罕见并发症,在神经影像学上可能表现为多灶性缺血。在药物相关性血管炎的情况下,大剂量皮质类固醇治疗可能会导致迅速改善,并最终解决相关的局灶性神经功能缺损。