Chowdhury Arnab, Griffith Megan P, Busse Eric, Pasha Ahmed Khurshid
Department of Hospital Medicine, Mayo Clinic Health System in Mankato, Mankato, MN, USA.
Department of Pathology, Mayo Clinic Health System in Mankato, Mankato, MN, USA.
Am J Case Rep. 2020 Dec 8;21:e925662. doi: 10.12659/AJCR.925662.
BACKGROUND Hemolytic uremic syndrome (HUS) develops from uncontrolled complement activation leading to intravascular hemolysis and thrombotic microangiopathy. Atypical HUS is diagnosed by excluding a disintegrin and metalloproteinase with thrombospondin type 1 motif, 13 deficiency, and infection-associated HUS. Patients with atypical HUS may respond to eculizumab. We present a case of a 67-year-old woman who developed atypical HUS with hemolytic anemia, renal failure, and thrombocytopenia following an elective hip arthroplasty. CASE REPORT An otherwise healthy 67-year-old woman was admitted to our hospital after an elective right total hip arthroplasty. In the postoperative course, she developed vomiting and acute renal failure that was initially attributed to a prerenal cause. She continued to have worsened renal failure in spite of intravenous hydration, and she also developed mild thrombocytopenia. A peripheral blood smear was performed and showed the presence of schistocytes (red blood cell fragments) consistent with microangiopathic hemolytic anemia. In the context of anemia, thrombocytopenia, and renal failure, this finding led to a prompt and early referral to a tertiary care center and a timely diagnosis of atypical HUS. The patient underwent treatment with plasmapheresis, hemodialysis, and eculizumab. CONCLUSIONS This report highlights the importance of examination of the peripheral blood smear in the diagnosis of thrombotic microangiopathy. As shown in our case, the presence of schistocytes indicates the need for prompt clinical management.
背景 溶血尿毒综合征(HUS)由不受控制的补体激活发展而来,导致血管内溶血和血栓性微血管病。非典型HUS通过排除具有血小板反应蛋白基序的去整合素和金属蛋白酶13缺乏症以及感染相关的HUS来诊断。非典型HUS患者可能对依库珠单抗有反应。我们报告一例67岁女性病例,该患者在择期髋关节置换术后出现非典型HUS,并伴有溶血性贫血、肾衰竭和血小板减少症。病例报告 一名67岁健康女性在择期行右侧全髋关节置换术后入住我院。在术后过程中,她出现呕吐和急性肾衰竭,最初归因于肾前性原因。尽管进行了静脉补液,她的肾衰竭仍持续恶化,并且还出现了轻度血小板减少症。进行了外周血涂片检查,结果显示存在与微血管病性溶血性贫血一致的裂体细胞(红细胞碎片)。在贫血、血小板减少症和肾衰竭的背景下,这一发现促使患者迅速转诊至三级医疗中心,并及时诊断为非典型HUS。该患者接受了血浆置换、血液透析和依库珠单抗治疗。结论 本报告强调了外周血涂片检查在血栓性微血管病诊断中的重要性。如我们的病例所示,裂体细胞的存在表明需要及时进行临床处理。