Department of Paediatric Surgery, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
Afr J Paediatr Surg. 2020 Jul-Dec;17(3 & 4):108-110. doi: 10.4103/ajps.AJPS_55_20.
Prune belly syndrome is an extremely rare congenital condition occurring predominantly in males. This triad syndrome comprises of partial or complete deficient abdominal wall muscles, undescended testes and dilated urinary collecting system. We present the case of a 2-year-old male patient, who presented with classic prune belly syndrome, operated with modification in classical Monfort technique of abdominoplasty. The basis of this approach was to save and use the supraumbilical abdominal wall which has better tensile strength. The infraumbilical skin was mostly discarded. The outcome was better in terms of cosmetic appearance as the scar was limited to the lower abdomen and better anterior abdominal wall strength.
脐膨出型腹壁发育不良症是一种极其罕见的先天性疾病，主要发生于男性。这种三联征包括部分或完全缺失的腹壁肌肉、未降睾丸和扩张的尿收集系统。我们介绍了一位 2 岁男性患者的病例，他患有典型的脐膨出型腹壁发育不良症，采用改良的经典蒙福特（Monfort）腹部整形术进行了手术。这种方法的基础是保存和使用具有更好拉伸强度的脐上腹壁。脐下皮肤大部分被丢弃。从美容外观的角度来看，结果更好，因为疤痕仅限于下腹部，并且前腹壁的强度更好。
