Matsukawa Toshihiro, Eguchi Katsuki, Nishino Ichizo, Okada Kohei, Oshimi Kazuo, Miyagishima Takuto
Department of Internal Medicine/Hematology Kushiro Rosai Hospital Kushiro Japan.
Department of Neurology Kushiro Rosai Hospital Kushiro Japan.
Clin Case Rep. 2020 Sep 8;8(12):2869-2873. doi: 10.1002/ccr3.3310. eCollection 2020 Dec.
Isolated amyloidosis, especially of amyloid light-chain type, is an infrequent disease. Systemic chemotherapy for light-chain amyloidosis isolated to skeletal muscles plays a key role to reduce clonal plasma cells producing aberrant immunoglobulin.
孤立性淀粉样变性,尤其是轻链型淀粉样变性,是一种罕见疾病。针对仅累及骨骼肌的轻链淀粉样变性进行全身化疗,对于减少产生异常免疫球蛋白的克隆性浆细胞起着关键作用。