Burgess L P, Quilligan J J, Moe R D, Lepore M L, Yim D W
Department of Surgery, Tripler (Hawaii), Army Medical Center.
Arch Otolaryngol Head Neck Surg. 1988 Feb;114(2):207-9. doi: 10.1001/archotol.1988.01860140105033.
A female newborn had a rare case of congenital multiple fibromatosis, consisting of multiple fibrous lesions that histologically resemble myofibromas. Bony and soft-tissue lesions usually undergo spontaneous resolution, but excision may be required if vital structures are compromised as was the case in this patient. When the lesions involve the viscera in a generalized form of the disease, the result is often fatal.
一名女新生儿患有一种罕见的先天性多发性纤维瘤病,由多个组织学上类似于肌纤维瘤的纤维性病变组成。骨和软组织病变通常会自行消退,但如果重要结构受到影响,如该患者的情况,则可能需要切除。当病变以疾病的全身性形式累及内脏时,结果往往是致命的。