Department of Neonatology, Cloudnine Hospital, Gurgaon, India
Department of Neonatology, Cloudnine Hospital, Gurgaon, India.
BMJ Case Rep. 2020 Dec 31;13(12):e236881. doi: 10.1136/bcr-2020-236881.
Haemophagocytic lymphohistiocytosis (HLH) is an aggressive syndrome which has characteristic symptoms and laboratory findings. Infection is a common trigger of HLH. We report a 2700 g male infant with persistent fever, massive hepatosplenomegaly and severe thrombocytopaenia. Laboratory evidence of primary dengue infection was detected. Investigations revealed hypertriglyceridaemia, hypofibrinogenaemia, hyperferritinaemia and elevated soluble CD25. Bone marrow examination revealed haemophagocytes. The diagnostic criteria for HLH were fulfilled. A diagnosis of secondary HLH triggered by primary dengue infection was considered. Dexamethasone was initiated and continued for 8 weeks. He responded clinically with regression of hepatosplenomegaly, was afebrile and platelet counts normalised. Dengue-associated HLH is often missed clinically as treating physicians focus more on the underlying infection and its treatment. In neonates, HLH should be considered as differential diagnosis of sepsis and other viral infections, particularly in situations of inappropriate response to standard management.
噬血细胞性淋巴组织细胞增生症(HLH)是一种侵袭性综合征,具有特征性的症状和实验室发现。感染是 HLH 的常见诱因。我们报告了一例 2700 克男性婴儿,其持续发热、巨大肝脾肿大和严重血小板减少。检测到原发性登革热感染的实验室证据。检查发现高甘油三酯血症、低纤维蛋白原血症、高铁蛋白血症和可溶性 CD25 升高。骨髓检查显示噬血细胞。符合 HLH 的诊断标准。考虑诊断为原发性登革热感染引起的继发性 HLH。给予地塞米松治疗,持续 8 周。他的临床症状有改善,肝脾肿大消退,无发热,血小板计数恢复正常。由于治疗医生更关注基础感染及其治疗,因此临床上常漏诊与登革热相关的 HLH。在新生儿中,HLH 应作为败血症和其他病毒感染的鉴别诊断,尤其是在对标准治疗无反应的情况下。