[伴有EWSR1-CREB1易位及局部区域微转移的原发性肺黏液样肉瘤]
[Primary pulmonary myxoid sarcoma associated with translocation EWSR1-CREB1 and locorregional micrometastases].
作者信息
Salazar Nicolás Alejandro, Oviedo Ramírez María Isabel, Salas Antón Clara
机构信息
Servicio de Anatomía Patológica, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, España.
Servicio de Anatomía Patológica, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, España.
出版信息
Rev Esp Patol. 2021 Jan-Mar;54(1):55-58. doi: 10.1016/j.patol.2019.02.006. Epub 2019 Apr 8.
Primary myxoid pulmonary sarcoma is a rare entity with an endobronchial growth. Although it should be included in the differential diagnosis of other sarcomas, its prognosis is usually favorable. We present the case of a 51-year-old patient with a mesenchymal tumor in the right lung, diagnosed as a primary pulmonary myxoid sarcoma, positive for EMA, vimentine and with a Ki-67 less than 5%; FISH revealed a EWSR1-CREB1 translocation.
原发性黏液样肺肉瘤是一种罕见的具有支气管内生长特点的疾病。尽管在其他肉瘤的鉴别诊断中应考虑到它，但它的预后通常较好。我们报告一例51岁患者，其右肺有一个间叶性肿瘤，诊断为原发性肺黏液样肉瘤，上皮膜抗原（EMA）、波形蛋白阳性，Ki-67小于5%；荧光原位杂交（FISH）显示有EWSR1-CREB1易位。
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