Solitary median maxillary central incisor syndrome: A rare entity.

Solitary median maxillary central incisor (SMMCI) syndrome is a complex disorder and a rare dental anomaly, which is estimated to occur in approximately 1:50,000 live births. It is a unique developmental abnormality which involves the central incisor tooth germs, occurring with or without systemic involvement; hence, its early diagnosis is of great importance. The objective of this study was to discuss a case of SMMCI syndrome and various dental treatment alternatives available in management of such cases. Due to the possible association of this syndrome with other developmental problems, an early diagnosis and management becomes important. Moreover, when it is associated with other developmental malformation and defects, the management becomes multidisciplinary.