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[Essential palatal myoclonus. A pediatric case report].

作者信息

Spini Roxana, Cohen Daniela, Juchli Marian, Ibarra Lilian

机构信息

División de Otorrinolaringología, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires.

División de Neurología, Hospital General de Niños Pedro de Elizalde, Ciudad Autónoma de Buenos Aires.

出版信息

Arch Argent Pediatr. 2021 Feb;119(1):e54-e57. doi: 10.5546/aap.2021.e54.

Abstract

Essential palatal myoclonus is a rare neurological disorder characterized by involuntary movements of the soft palate musculature causing objective-clicking tinnitus. The palatal myoclonus is classified in two forms, secondary and essential palatal myoclonus. Primary (essential) palatal myoclonus is the most common type in childhood. Normal computed tomography and magnetic resonance guide the diagnosis. Spontaneous resolution usually occurs in the essential type of palatal myoclonus. In this report, we present an 8-year-old child making rhythmic, rapid clicking noises from her throat with spontaneous resolution.

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