Nephrology, CUB Erasme, Brussels, Belgium.
Radiology, UZ Brussel, Brussels, Belgium.
BMJ Case Rep. 2021 Jan 18;14(1):e237331. doi: 10.1136/bcr-2020-237331.
We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.
我们描述了一例 35 岁女性患者,患有全身性纵隔和腹部淋巴管瘤病,并伴有蛋白丢失性肠病,当开始使用西罗莫司治疗后,病情得到了成功改善。