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系统性全身淋巴管瘤病：病因不明，治疗极具挑战。

Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat.

机构信息

Nephrology, CUB Erasme, Brussels, Belgium.

Radiology, UZ Brussel, Brussels, Belgium.

出版信息

BMJ Case Rep. 2021 Jan 18;14(1):e237331. doi: 10.1136/bcr-2020-237331.

DOI:10.1136/bcr-2020-237331
PMID:33462010
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7813405/
Abstract

We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.

摘要

我们描述了一例 35 岁女性患者，患有全身性纵隔和腹部淋巴管瘤病，并伴有蛋白丢失性肠病，当开始使用西罗莫司治疗后，病情得到了成功改善。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d01/7813405/3e2c84fcf841/bcr-2020-237331f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d01/7813405/3e2c84fcf841/bcr-2020-237331f01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4d01/7813405/3e2c84fcf841/bcr-2020-237331f01.jpg

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Successful treatment of diffuse pulmonary lymphangiomatosis with sirolimus.西罗莫司成功治疗弥漫性肺淋巴管瘤病
Respir Med Case Rep. 2020 Feb 1;29:101014. doi: 10.1016/j.rmcr.2020.101014. eCollection 2020.
2
Volumetric analysis at abdominal CT: oncologic and non-oncologic applications.腹部CT的容积分析：肿瘤学和非肿瘤学应用
Br J Radiol. 2019 Mar;92(1095):20180631. doi: 10.1259/bjr.20180631. Epub 2018 Nov 30.
3
Targeted therapy in patients with PIK3CA-related overgrowth syndrome.PIK3CA 相关过度生长综合征患者的靶向治疗。
J Dev Biol. 2022 Feb 8;10(1):11. doi: 10.3390/jdb10010011.
Nature. 2018 Jun;558(7711):540-546. doi: 10.1038/s41586-018-0217-9. Epub 2018 Jun 13.
4
Abdominal cystic lymphangioma in a term newborn: A case report and update of new treatments.足月儿腹部囊性淋巴管瘤：一例报告及新治疗方法的更新
Medicine (Baltimore). 2017 Feb;96(8):e5984. doi: 10.1097/MD.0000000000005984.
5
Sirolimus in the Treatment of Vascular Anomalies.西罗莫司在血管异常治疗中的应用
Eur J Pediatr Surg. 2017 Feb;27(1):86-90. doi: 10.1055/s-0036-1593383. Epub 2016 Oct 10.
6
Primary intestinal lymphangiomatosis of the ileum in an adult-the role of surgical approach.成人回肠原发性肠淋巴管瘤病——手术方法的作用
J Surg Case Rep. 2016 Aug 17;2016(8):rjw133. doi: 10.1093/jscr/rjw133.
7
Emergency presentation of cystic lymphangioma of the colon: A case report and literature review.结肠囊性淋巴管瘤的急诊表现：一例报告及文献复习
Int J Surg Case Rep. 2016;24:162-5. doi: 10.1016/j.ijscr.2016.05.045. Epub 2016 May 27.
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