网状浅表淋巴管畸形

Net-like superficial lymphatic malformation.

作者信息

Iznardo Helena, Baselga Eulalia, Mozos Anna, Szafranska Justyna, Orellana-Fernández Ruth, Roé Esther

机构信息

Department of Dermatology, Hospital de la Santa Creu i Sant Pau, Universitat Autònoma de Barcelona, Barcelona, Spain.

Department of Dermatology, Hospital Sant Joan de Déu, Esplugues de Llobregat, Barcelona, Spain.

出版信息

Pediatr Dermatol. 2021 Mar;38(2):516-517. doi: 10.1111/pde.14526. Epub 2021 Jan 24.

DOI:10.1111/pde.14526

PMID:33486776

Abstract

The net-like superficial lymphatic malformation (LM) is a newly described entity with distinctive clinical, dermoscopic, and histologic characteristics. Clinical picture consists of red to purplish macules with a finely reticulated pattern of vascular structures. Dermoscopy shows arborizing telangiectatic vessels. Histology is characterized by a vascular proliferation composed of thin-walled vessels, located in the upper dermis, that stains positive with podoplanin (D2-40). We report a new case of LM with an additional clinical feature, hypopigmented areas.

摘要

网状浅表淋巴管畸形（LM）是一种新描述的疾病，具有独特的临床、皮肤镜和组织学特征。临床表现为红色至紫色斑疹，伴有血管结构的精细网状图案。皮肤镜显示树枝状扩张的毛细血管。组织学特征为位于真皮上层的由薄壁血管组成的血管增生，对足突蛋白（D2-40）染色呈阳性。我们报告一例具有额外临床特征——色素减退区域的LM新病例。