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在一名努南综合征患儿中同期进行室间隔肌切除术和二尖瓣修复术。

Concomitant septal myectomy and mitral valve repair in a child with Noonan syndrome.

作者信息

Doi Toshio, Toritsuka Daisuke, Higashida Akihiko, Yokoyama Shigeki, Fukahara Kazuaki, Yoshimura Naoki

机构信息

First Department of Surgery University of Toyama Toyama Japan.

出版信息

Clin Case Rep. 2020 Nov 18;9(1):367-370. doi: 10.1002/ccr3.3531. eCollection 2021 Jan.

DOI:10.1002/ccr3.3531
PMID:33489184
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7813065/
Abstract

We successfully performed concomitant septal myectomy and mitral valve repair in a child with Noonan syndrome.

摘要

我们成功地为一名患有努南综合征的儿童实施了同期室间隔心肌切除术和二尖瓣修复术。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/71c3904d6146/CCR3-9-367-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/8f70d32facb7/CCR3-9-367-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/0ac4319fe9f1/CCR3-9-367-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/71c3904d6146/CCR3-9-367-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/8f70d32facb7/CCR3-9-367-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/0ac4319fe9f1/CCR3-9-367-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bf65/7813065/71c3904d6146/CCR3-9-367-g003.jpg

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本文引用的文献

1
Early Outcomes of Cardiac Surgery in Patients with Noonan Syndrome.努南综合征患者心脏手术的早期结果。
Semin Thorac Cardiovasc Surg. 2019 Autumn;31(3):507-513. doi: 10.1053/j.semtcvs.2018.12.004. Epub 2018 Dec 18.
2
Isolated septal myectomy for hypertrophic obstructive cardiomyopathy: an update on the Toronto General Hospital experience.肥厚性梗阻性心肌病的孤立性室间隔心肌切除术:多伦多综合医院经验的最新进展
Ann Cardiothorac Surg. 2017 Jul;6(4):364-368. doi: 10.21037/acs.2017.05.12.
3
Mitral Regurgitation in Patients With Hypertrophic Obstructive Cardiomyopathy: Implications for Concomitant Valve Procedures.
肥厚型梗阻性心肌病患者的二尖瓣反流:对同期瓣膜手术的影响。
J Am Coll Cardiol. 2016 Oct 4;68(14):1497-504. doi: 10.1016/j.jacc.2016.07.735.
4
Surgical Ventricular Septal Myectomy for Patients With Noonan Syndrome and Symptomatic Left Ventricular Outflow Tract Obstruction.为患有努南综合征和有症状的左心室流出道梗阻患者实施外科室间隔心肌切除术。
Am J Cardiol. 2015 Oct 1;116(7):1116-21. doi: 10.1016/j.amjcard.2015.06.037. Epub 2015 Jul 16.
5
Cardiovascular disease in Noonan syndrome.努南综合征相关心血管疾病
Arch Dis Child. 2014 Jul;99(7):629-34. doi: 10.1136/archdischild-2013-305047. Epub 2014 Feb 17.
6
Noonan syndrome.努南综合征。
Lancet. 2013 Jan 26;381(9863):333-42. doi: 10.1016/S0140-6736(12)61023-X. Epub 2013 Jan 10.
7
Survival implications: hypertrophic cardiomyopathy in Noonan syndrome.生存意义:努南综合征中的肥厚型心肌病。
Congenit Heart Dis. 2011 Jan-Feb;6(1):41-7. doi: 10.1111/j.1747-0803.2010.00465.x.
8
Sustained improvement after combined anterior mitral valve leaflet retention plasty and septal myectomy in preventing systolic anterior motion in hypertrophic obstructive cardiomyopathy in children.联合二尖瓣前叶保留成形术和室间隔心肌切除术在预防儿童肥厚型梗阻性心肌病收缩期前向运动中的持续改善。
Eur J Cardiothorac Surg. 2009 Sep;36(3):546-52. doi: 10.1016/j.ejcts.2009.03.049. Epub 2009 May 22.
9
Modified surgical techniques and long-term outcome of mitral valve reconstruction in 111 children.111例儿童二尖瓣重建的改良手术技术及长期疗效
Ann Thorac Surg. 2008 Aug;86(2):604-13. doi: 10.1016/j.athoracsur.2008.03.026.
10
Long-term effects of surgical septal myectomy on survival in patients with obstructive hypertrophic cardiomyopathy.外科室间隔心肌切除术对梗阻性肥厚型心肌病患者生存的长期影响。
J Am Coll Cardiol. 2005 Aug 2;46(3):470-6. doi: 10.1016/j.jacc.2005.02.090.