Nakajima Rie, Togo Atsuko, Kanno Yasuhira, Hayashi Masaru, Mitsuzuka Kanako, Ishimoto Hitoshi
Department of Obstetrics and Gynecology, Specialized Clinical Science, Tokai University School of Medicine, Japan.
Case Rep Obstet Gynecol. 2020 Dec 28;2020:8854676. doi: 10.1155/2020/8854676. eCollection 2020.
We report a case of acquired factor XI deficiency with lupus anticoagulant (LA) in a 28-year-old primigravida who presented with finger pain and eruptions on her palms and fingers during the 3rd trimester of pregnancy. The patient complained of pain and reddening of the fingers at 30 weeks of gestation. She was referred to our tertiary center with a diagnosis of preeclampsia and suspected collagen disease at 35 weeks of gestation. Erythema was seen on the fingers and palms, and she presented with pain and cryesthesia on the fingers. Laboratory investigations revealed an activated partial thromboplastin time of 51 s (normal, 23-40 s), although it was normal during the 30th and 34th gestational weeks, LA with an anticardiolipin-beta2-glycoprotein I complex antibody, and low level of clotting XI activity (25 U/mL). On week 37 day 0 of gestation, the patient presented with severe hypertension. An urgent Cesarean section was performed after transfusion of two units of fresh frozen plasma. There was no excessive bleeding during the surgery or the postpartum period. The symptoms on her fingers and palms gradually improved after surgery. Our case indicates that dermatoses of pregnancy may become a starting point for the diagnosis of autoimmune diseases and coagulation abnormalities. When a patient presents with an atypical symptom, as in our case, the possibility of various diseases should be considered.
我们报告了一例28岁初产妇获得性因子XI缺乏合并狼疮抗凝物(LA)的病例,该患者在妊娠晚期出现手指疼痛以及手掌和手指皮疹。患者在妊娠30周时出现手指疼痛和发红。妊娠35周时,她因子痫前期诊断及疑似胶原病转诊至我们的三级中心。手指和手掌可见红斑,手指有疼痛和感觉异常。实验室检查显示活化部分凝血活酶时间为51秒(正常为23 - 40秒),尽管在妊娠第30周和第34周时该指标正常,存在抗心磷脂-β2-糖蛋白I复合物抗体的LA,且凝血因子XI活性水平低(25 U/mL)。妊娠37周0天时,患者出现严重高血压。输注两单位新鲜冰冻血浆后紧急行剖宫产。手术期间及产后均无过度出血。术后其手指和手掌症状逐渐改善。我们的病例表明,妊娠皮肤病可能成为自身免疫性疾病和凝血异常诊断的起点。当患者出现非典型症状时,如我们的病例,应考虑各种疾病的可能性。