Thakur Surekha, Saha S C, Sikka Pooja, Das Chandan Krushna, Arpitha Kollabathula, Thakur Uttam Kumar
Department of Obstetrics and Gynecology, PGIMER, Chandigarh, India.
Medical Oncology Regional Cancer Centre, PGIMER, Chandigarh, India.
Gynecol Oncol Rep. 2020 Dec 31;35:100693. doi: 10.1016/j.gore.2020.100693. eCollection 2021 Feb.
The term DSD (Disorders of Sex development) is issued to define those conditions in whom disharmony exists between chromosomal, hormonal and anatomical sex. Parental and patient mental health and quality of life are adversely affected by these conditions. Moreover, individuals with an underlying DSD, especially those with specific Y chromosomal material in their karyotype have an increased risk for developing a germ cell tumor. Here, we present a unique case of 46XY DSD with bilateral dysgerminomas presenting with abdominal mass at the age of 24 years, who was treated with one cycle of chemotherapy comprising of Carboplatin and Etoposide, following which he developed tumor lysis syndrome and later underwent exploratory laparotomy.
性发育障碍(DSD)这一术语用于定义那些染色体、激素和解剖学性别之间存在不协调的情况。这些情况会对父母和患者的心理健康及生活质量产生不利影响。此外,患有潜在性发育障碍的个体,尤其是那些核型中含有特定Y染色体物质的个体,发生生殖细胞肿瘤的风险会增加。在此,我们报告一例独特的46XY性发育障碍病例,该患者24岁时双侧无性细胞瘤伴腹部肿块,接受了一个周期由卡铂和依托泊苷组成的化疗,化疗后发生肿瘤溶解综合征,随后接受了剖腹探查术。