Department of Thoracic Surgery, Wuxi Lung Transplant Center, Wuxi People's Hospital Affiliated to Nanjing Medical University, Wuxi, China.
Department of Cardiovascular Surgery, Wuxi People's Hospital Affiliated to Nanjing Medical University, Wuxi, China.
J Card Surg. 2021 Apr;36(4):1560-1562. doi: 10.1111/jocs.15360. Epub 2021 Jan 24.
Optimal surgical treatment for Eisenmenger syndrome in adult congenital heart disease remains in debate.
We report a case of a 22-year-old female with Eisenmenger syndrome secondary to ventricular septum defect (VSD), who underwent cardiac defect closure combined with bilateral lung transplantation in our center. The patient had an uncorrected peri-membranous VSD and subsequently developed severe pulmonary hypertension. We patched the defect under cardiopulmonary bypass. Then a sequential bilateral lung transplantation was performed with venoarterial extracorporeal membrane oxygenation support. The patient had a good postoperative recovery and remained well at follow-up at 1 year. To conclude, cardiac defect repair combined bilateral lung transplantation may be a feasible option for selected patients with Eisenmenger Syndrome.
成人先天性心脏病合并艾森曼格综合征的最佳手术治疗仍存在争议。
我们报告了一例 22 岁女性患者，因室间隔缺损（VSD）继发艾森曼格综合征，在我院行心脏缺损修补术联合双侧肺移植术。患者存在未矫正的膜周部 VSD，随后发展为严重的肺动脉高压。我们在体外循环下修补了该缺损。然后在体外膜氧合支持下进行序贯双侧肺移植术。患者术后恢复良好，随访 1 年情况良好。总之，心脏缺损修补术联合双侧肺移植术可能是治疗艾森曼格综合征的一种可行选择。
