Yadav Ajay Kumar, Sharma Mohit, Puj Ketul
The Gujarat Cancer & Research Institute, Ahmedabad, Gujarat India.
Indian J Thorac Cardiovasc Surg. 2021 Jul;37(4):463-466. doi: 10.1007/s12055-020-01095-9. Epub 2021 Jan 28.
Soft tissue aneurysmal bone cysts (STABCs) are extremely rare extraosseous counterpart of aneurysmal bone cyst (ABC), with close resemblance to histo-morphologic characteristics of ABC. Here we would like to report a 13-year-old female patient, who presented with a large mass, occupying the entire left hemithorax. Patient underwent resection of the thoracic mass. On histopathological examination, it was found to be a soft tissue ABC. It is a very rare tumor and until date 28 cases have been reported in English literature, to the best of our knowledge. On review of the literature, we found this to be the first case of STABC reported in thoracic cavity. The objective of this case presentation is to provide information regarding clinical presentation, radiological and pathological features, and course of management for this rare disease. Soft tissue ABCs are a new class of tumors, so more extensive research is required to establish standard guidelines for their diagnosis and management, to yield better prognosis.
软组织动脉瘤样骨囊肿（STABCs）是动脉瘤样骨囊肿（ABC）极为罕见的骨外对应物，在组织形态学特征上与ABC极为相似。在此，我们报告一名13岁女性患者，她因一个占据整个左半胸的巨大肿块前来就诊。患者接受了胸部肿块切除术。经组织病理学检查，发现其为软组织ABC。这是一种非常罕见的肿瘤，据我们所知，迄今为止英文文献中仅报道了28例。在查阅文献时，我们发现这是胸腔内报道的首例STABC病例。本病例报告的目的是提供有关这种罕见疾病的临床表现、放射学和病理学特征以及治疗过程的信息。软组织ABC是一类新的肿瘤，因此需要更广泛的研究来建立其诊断和治疗的标准指南，以获得更好的预后。
