DMU Smart Imaging, Medical Imaging and Interventional Radiology Department, Assistance Publique-Hôpitaux de Paris, GH Université Paris-Saclay, Ambroise Paré Hospital, Boulogne-Billancourt, France.
DMU Smart Imaging, Medical Imaging and Interventional Radiology Department, Assistance Publique-Hôpitaux de Paris, GH Université Paris-Saclay, Antoine Béclère Hospital, Clamart, France.
Ann Vasc Surg. 2021 May;73:538-541. doi: 10.1016/j.avsg.2020.12.030. Epub 2021 Feb 4.
Intercostal artery aneurysms are extremely rare, and could be associated with aortic coarctation, systemic diseases like neurofibromatosis, or more rarely Marfan syndrome. They could be life-threatening when ruptured, leading to hemothorax or mediastinal hematoma. Endovascular management before or after rupture of intercostal aneurysms, should be considered. Radiculomedullary branch, especially Adamkiewicz one, emanating from intercostal artery needs special focus during endovascular management, to avoid spinal cord ischemia. We present herein the first case of a ruptured intercostal artery aneurysm with a downstream Adamkiewicz artery in a suspected Marfan patient. Aneurysmal exclusion using stent graft was the unique therapeutic option.
肋间动脉动脉瘤极为罕见,可能与主动脉缩窄、神经纤维瘤病等系统性疾病有关,或更罕见的马凡综合征有关。当破裂时,它们可能会导致危及生命的血胸或纵隔血肿。在肋间动脉瘤破裂前或破裂后应考虑血管内治疗。肋间动脉发出的脊神经根髓支,特别是 Adamkiewicz 动脉,在血管内治疗期间需要特别关注,以避免脊髓缺血。我们在此报告首例疑似马凡综合征患者的破裂性肋间动脉动脉瘤伴下游 Adamkiewicz 动脉病例。使用支架移植物进行动脉瘤排除是唯一的治疗选择。