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婴儿期经前路成功手术修复动脉干合并主动脉弓中断。

Successful surgical repair of truncus arteriosus with interrupted aortic arch in infancy by an anterior approach.

作者信息

Fujiwara K, Yokota Y, Okamoto F, Kiyota Y, Sugawara E, Iemura J, Makino S

机构信息

Department of Cardiovascular Surgery, Hyogo Kenritsu Amagasaki Hospital, Hyogo, Japan.

出版信息

Ann Thorac Surg. 1988 Apr;45(4):441-4. doi: 10.1016/s0003-4975(98)90021-2.

DOI:10.1016/s0003-4975(98)90021-2
PMID:3355287
Abstract

A 98-day-old infant was successfully operated on for truncus arteriosus (type I) with interrupted aortic arch (type B) using a one-stage anterior approach. The interrupted aortic arch was reconstructed by direct anastomosis between the ascending and descending aorta. The ventricular septal defect was closed, and a 12-mm porcine valved conduit was placed on the right side of the ascending aorta to establish continuity between the right ventricle and pulmonary artery. Surgical procedures for the repair of this malformation are the focus of discussion.

摘要

一名98天大的婴儿接受了一期前路手术,成功修复了I型共同动脉干合并B型主动脉弓中断。通过升主动脉与降主动脉直接吻合重建中断的主动脉弓。室间隔缺损得以闭合,并在升主动脉右侧置入一根12毫米带瓣猪导管,以建立右心室与肺动脉之间的连接。修复这种畸形的外科手术是讨论的焦点。

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