Piezo1-xerocytosis red cell metabolome shows impaired glycolysis and increased hemoglobin oxygen affinity.
作者信息
Kiger Laurent, Oliveira Lydie, Guitton Corinne, Bendélac Laurence, Ghazal Kaldoun, Proulle Valérie, Galacteros Frédéric, Junot Christophe, Fenaille François, Roméo Paul-Henri, Garçon Loic, Picard Véronique
机构信息
Université Paris Est Creteil, INSERM Unité U955, Institut Mondor de Recherche Biomédicale (IMRB), Creteil, France.
Laboratoire d'Excellence GR-Ex, Université Paris, Descartes, France.
出版信息
Blood Adv. 2021 Jan 12;5(1):84-88. doi: 10.1182/bloodadvances.2020003028.
Abstract
摘要
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本文引用的文献
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Haematologica. 2020 Jun;105(6):e268-e271. doi: 10.3324/haematol.2019.231159. Epub 2019 Oct 17.
2
PIEZO1 activation delays erythroid differentiation of normal and hereditary xerocytosis-derived human progenitor cells.机械敏感离子通道蛋白 1（PIEZO1）的激活可延迟正常和遗传性先天性非球形细胞性溶血性贫血（hereditary xerocytosis）衍生的人祖细胞的红系分化。
Haematologica. 2020 Mar;105(3):610-622. doi: 10.3324/haematol.2019.218503. Epub 2019 Aug 14.
3
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4
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Haematologica. 2019 Aug;104(8):1554-1564. doi: 10.3324/haematol.2018.205328. Epub 2019 Jan 17.
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