Suppr超能文献

罕见肌肉骨骼和神经肌肉疾病的疼痛表型。

Pain Phenotypes in Rare Musculoskeletal and Neuromuscular Diseases.

机构信息

Department of Anesthesiology, Critical Care and Pain Medicine, Boston Children's Hospital, Harvard Medical School, Boston, MA, 02115, USA.

Department of Radiology, Brigham and Women's Hospital, Boston, MA, 02115, USA.

出版信息

Neurosci Biobehav Rev. 2021 May;124:267-290. doi: 10.1016/j.neubiorev.2021.02.009. Epub 2021 Feb 10.

Abstract

For patients diagnosed with a rare musculoskeletal or neuromuscular disease, pain may transition from acute to chronic; the latter yielding additional challenges for both patients and care providers. We assessed the present understanding of pain across a set of ten rare, noninfectious, noncancerous disorders; Osteogenesis Imperfecta, Ehlers-Danlos Syndrome, Achondroplasia, Fibrodysplasia Ossificans Progressiva, Fibrous Dysplasia/McCune-Albright Syndrome, Complex Regional Pain Syndrome, Duchenne Muscular Dystrophy, Infantile- and Late-Onset Pompe disease, Charcot-Marie-Tooth Disease, and Amyotrophic Lateral Sclerosis. Through the integration of natural history, cross-sectional, retrospective, clinical trials, & case studies we described pathologic and genetic factors, pain sources, phenotypes, and lastly, existing therapeutic approaches. We highlight that while rare diseases possess distinct core pathologic features, there are a number of shared pain phenotypes and mechanisms that may be prospectively examined and therapeutically targeted in a parallel manner. Finally, we describe clinical and research approaches that may facilitate more accurate diagnosis, monitoring, and treatment of pain as well as elucidation of the evolving nature of pain phenotypes in rare musculoskeletal or neuromuscular illnesses.

摘要

对于诊断患有罕见肌肉骨骼或神经肌肉疾病的患者,疼痛可能会从急性转为慢性;后者给患者和护理人员带来了额外的挑战。我们评估了对一组十种罕见的非传染性、非癌症疾病的疼痛的现有理解;成骨不全症、埃勒斯-当洛斯综合征、软骨发育不全症、进行性骨化性纤维发育不良、纤维性骨发育不良/麦-卡恩综合征、复杂区域疼痛综合征、杜氏肌营养不良症、婴儿和迟发性庞贝病、遗传性运动感觉神经病和肌萎缩侧索硬化症。通过自然病史、横断面、回顾性、临床试验和病例研究的综合分析,我们描述了病理和遗传因素、疼痛来源、表型,最后是现有的治疗方法。我们强调,虽然罕见疾病具有独特的核心病理特征,但存在许多共同的疼痛表型和机制,可以以并行的方式进行前瞻性检查和治疗。最后,我们描述了临床和研究方法,这些方法可以促进更准确的疼痛诊断、监测和治疗,以及阐明罕见肌肉骨骼或神经肌肉疾病中疼痛表型的演变性质。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/dab1/9521731/6d74caf68859/nihms-1838510-f0001.jpg

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验