Tatekawa Yukihiro
Department of Pediatric Surgery, Saku Central Hospital Advanced Care Center, 3400-28, Nakagomi, Saku-shi, Nagano 385-0051, Japan.
J Surg Case Rep. 2021 Feb 10;2021(2):rjaa608. doi: 10.1093/jscr/rjaa608. eCollection 2021 Feb.
We report herein a patient with a cloacal malformation and an absent vagina. The patient underwent colostomy on Day 1 of life. At 7 months of age, fistulography of the cloaca showed a common channel >3 cm in length; a vagina was not visible. At the age of 11 months, the patient underwent abdominoperineal anoplasty with the repurposing of her rectal fistula as a substitute vagina. Intraoperative examination revealed a bicornuate uterus and bilateral ovaries. The rectum was resected 7 cm at the confluence of the cloaca. The colonic stump was pulled through a newly created anal canal and an anoplasty was performed. Two months after this procedure, the patient experienced anal prolapse. At the age of 17 months, she underwent partial urogenital mobilization and a modified Delorme operation, and 5 months later the colostomy was closed. At present, this patient is 3 years old and doing well.
我们在此报告一名患有泄殖腔畸形且无阴道的患者。该患者在出生第1天接受了结肠造口术。7个月大时,泄殖腔瘘管造影显示共同通道长度大于3厘米;未发现阴道。11个月大时,患者接受了腹会阴肛门成形术,将直肠瘘重新用作替代阴道。术中检查发现双子宫和双侧卵巢。在泄殖腔汇合处切除直肠7厘米。将结肠残端经新造肛管拖出并进行肛门成形术。此手术后两个月,患者出现肛门脱垂。17个月大时,她接受了部分泌尿生殖系统游离术和改良的德洛姆手术,5个月后结肠造口关闭。目前,这名患者3岁,情况良好。