Ahmad Ali, El-Am Edward A, Kurmann Reto D, Hagler Donald J, Bois Melanie C, Maleszewski Joseph J, Klarich Kyle W
Department of Cardiovascular Medicine, Mayo Clinic, Rochester, MN, United States.
Department of Medicine, Indiana University School of Medicine, Indianapolis, IN, United States.
Front Cardiovasc Med. 2021 Jan 27;7:624219. doi: 10.3389/fcvm.2020.624219. eCollection 2020.
Cardiac papillary fibroelastomas (PFEs) are the most common primary benign cardiac tumors, although they are somewhat unusual in children and typically seen on the left-sided cardiac valves. A 10-week-old patient was found to have a partial atrioventricular canal defect, with associated tricuspid and mitral regurgitation. He was medically managed until 1 year of age, when surgical correction was done. During the procedure, a PFE was found incidentally on the TV. This is one of the youngest patients to be reported with PFE, thus adding to the literature of these unusual cases in children.
心脏乳头肌纤维弹性瘤(PFEs)是最常见的原发性心脏良性肿瘤,尽管在儿童中较为少见,且通常见于左侧心脏瓣膜。一名10周大的患者被发现患有部分房室通道缺损,并伴有三尖瓣和二尖瓣反流。他在1岁前接受药物治疗,1岁时进行了手术矫正。手术过程中,偶然在三尖瓣上发现了一个心脏乳头肌纤维弹性瘤。这是有报道的患有心脏乳头肌纤维弹性瘤的最年幼患者之一,从而丰富了儿童此类罕见病例的文献资料。