Satish Kumar Lakshmi, Kaundinya Kiran B
Bahrain Defence Force Hospital, Bahrain.
Int J Surg Case Rep. 2021 Mar;80:105652. doi: 10.1016/j.ijscr.2021.105652. Epub 2021 Feb 15.
Wilkie's syndrome[SMA(Superior Mesenteric Artery) syndrome or Cast syndrome]) is a unique and rare presentation which may be included in the differential diagnosis especially when a Gastric outlet obstruction is being investigated and there is a history of an associated element of rapid weight loss. The purpose of presenting this case report is its uniqueness given a history of intermittent fasting rather than the usual eating disorders.
A crescendo worsening of symptoms of intractable vomiting, inability to eat, upper abdominal gas bloating and post meal abdominal pain since one week in a patient during a period of fasting for the first time had been observed.
After initial resuscitation, an ultrasound abdomen and an abdominal x ray revealed a distended stomach and a nasogastric tube was immediately introduced to avoid aspiration. A CT scan of the abdomen with contrast revealed the compressed duodenum in the aortomesenteric angle and the diagnosis of SMA syndrome was confirmed. An upper gastrointestinal endoscopy was also done to rule out other causes and it was found to be normal.
In an acute presentation, the response to conservative management is remarkable and in the absence of any possible future reoccurrences the surgical options may be avoided. High index of suspicion, appropriate radiological diagnosis and stepwise treatment options may guide the troubled patient towards recovery in this rare presentation. A proper history taking is key in diagnosing such a condition and does not have to be limited to eating disorders, typically.
威尔基综合征([肠系膜上动脉综合征或卡斯综合征])是一种独特且罕见的病症,在鉴别诊断中可能会被考虑,尤其是在对胃出口梗阻进行检查且有快速体重减轻相关病史的情况下。呈现此病例报告的目的在于其独特性,因为该病例有间歇性禁食史而非常见的饮食失调史。
首次观察到一名患者在禁食期间,自一周以来顽固性呕吐、无法进食、上腹部胀气和餐后腹痛症状逐渐加重。
初始复苏后,腹部超声和腹部X线检查显示胃扩张,立即插入鼻胃管以避免误吸。腹部增强CT扫描显示十二指肠在主动脉肠系膜角处受压,确诊为肠系膜上动脉综合征。还进行了上消化道内镜检查以排除其他病因,结果正常。
在急性发作时,保守治疗的效果显著,若不存在未来复发的可能性,可避免手术选择。高度的怀疑指数、恰当的影像学诊断和逐步的治疗方案可引导此类罕见病症的患者康复。通常,详细的病史采集是诊断此类病症的关键,且不必局限于饮食失调。