表现为腰骶坐骨神经综合征的原发性硬化性上皮样纤维肉瘤：病例报告及文献复习
Primary sclerosing epithelioid fibrosarcoma presenting as lombosciatic syndrome: Case report and literature review.
作者信息
Khezami Karim, Gharbi Ahmed, Chabaane Mohamed, Bennour Mohamed Amine, Nouri Habib
机构信息
Faculty of Medicine of Tunis, University Tunis El Manar, Department of Orthopedic Surgery, Habib Bougatfa Hospital, Bizerte, Tunisia.
出版信息
Int J Surg Case Rep. 2021 Mar;80:105657. doi: 10.1016/j.ijscr.2021.105657. Epub 2021 Feb 18.
INTRODUCTION AND IMPORTANCE
Sclerosing epithelioid fibrosarcoma (SEF) is a rare variant of low grade fibrosarcoma, with specific histological and immunohistochemical features. SEF is a difficult to diagnose. The prognosis is poor with a 40% mortality rate.
CASE PRESENTATION
We report a case of 45-year-old female patient who presented to our department with a history of right sciatalgia evolving for three months. On physical examination, a firmly not well-defined mass was found in the right gluteal region. The histological diagnosis revealed a SEF.
CLINICAL DISCUSSION
SEF appears to be a slowly growing tumor often present for several months or years before diagnosis. The 3-month delay of our diagnosis shows the difficulty arising from the inconclusive clinical of this tumor.
CONCLUSION
SEF of the gluteal region can induce sciatalgia. The diagnosis should be made as early as possible in order to improve the prognosis.
引言与重要性
硬化性上皮样纤维肉瘤（SEF）是低级别纤维肉瘤的一种罕见变体，具有特定的组织学和免疫组化特征。SEF难以诊断。其预后较差，死亡率为40%。
病例报告
我们报告一例45岁女性患者，因右坐骨神经痛病史3个月前来我院就诊。体格检查发现右侧臀区有一质地硬、边界不清的肿块。组织学诊断为SEF。
临床讨论
SEF似乎是一种生长缓慢的肿瘤，在诊断前通常已存在数月或数年。我们的诊断延迟了3个月，这表明该肿瘤不确定的临床表现会带来诊断困难。
结论
臀区SEF可诱发坐骨神经痛。应尽早做出诊断以改善预后。
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