Department of General Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Department of Pediatrics, Advanced Pediatric Centre, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Ann R Coll Surg Engl. 2021 Mar;103(3):e94-e97. doi: 10.1308/rcsann.2020.7037.
Behçet's disease is a rare disease characterised by recurrent oral ulcers, with systemic manifestations including genital ulcers, ocular disease, skin lesions, gastrointestinal disease, neurologic disease, vascular disease and arthritis. Most clinical manifestations of Behçet's disease are believed to be due to vasculitis. The heterogeneous clinical spectrum is influenced by sex, ethnicity and country of residence. Vascular manifestation in the form of isolated large brachial artery aneurysm is rare in children. Treatment involves aneurysmorrhaphy to avoid rupture or ischaemic sequelae in addition to lifelong medical management to control vasculitis.
贝赫切特病是一种罕见的疾病,其特征为反复发作的口腔溃疡,伴有全身表现,包括生殖器溃疡、眼部疾病、皮肤损伤、胃肠道疾病、神经系统疾病、血管疾病和关节炎。大多数贝赫切特病的临床表现被认为是由于血管炎引起的。其异质性的临床谱受性别、种族和居住国的影响。以孤立性大型肱动脉动脉瘤形式出现的血管表现在儿童中较为罕见。治疗包括动脉瘤修复术,以避免破裂或缺血性后遗症,此外还需要终身进行医学管理以控制血管炎。