Gotor M A, Medrano J, Ruiz C, Alfonso E R, Guerrero J, de Gregorio M A
Sección de Neumología, Hospital de Calatayud, Zaragoza.
Arch Bronconeumol. 1997 Dec;33(11):591-3. doi: 10.1016/s0300-2896(15)30519-6.
Behcet's disease in a 27-year-old male is described. The patient presented fever, dyspnea and hemoptysis. A chest X-ray revealed right hilar enlargement. Exploratory thoracotomy revealed a pulsating mass in the superior lobar artery consistent with aneurysm. Pulmonary biopsy confirmed necrotizing vasculitis of the tissue consistent with Behcet's disease. Pulmonary arteriography showed and aneurysmatic enlargement of the bifurcation between the mid and righ inferior lobar arteries, with thrombosis of the upper right and lower left lobar arteries. Resolution of symptoms was achieved through treatment with corticoids and azathioprine.
本文描述了一名27岁男性的白塞病病例。该患者出现发热、呼吸困难和咯血症状。胸部X线检查显示右肺门增大。开胸探查发现上叶动脉有一个搏动性肿块,符合动脉瘤表现。肺活检证实组织坏死性血管炎,符合白塞病。肺动脉造影显示中叶与右下叶动脉分叉处动脉瘤样扩张,右上叶和左下叶动脉血栓形成。通过使用皮质类固醇和硫唑嘌呤治疗,症状得到缓解。