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先天性听小骨异常:68例病例回顾

Congenital ossicular abnormalities: a review of 68 cases.

作者信息

Cousins V C, Milton C M

机构信息

Institute of Laryngology and Otology London.

出版信息

Am J Otol. 1988 Jan;9(1):76-80.

PMID:3364539
Abstract

Sixty-eight cases of congenital conductive hearing loss due to ossicular abnormalities were reviewed. The clinical and surgical details of each case were documented, and a classification was drawn up on the basis of the abnormalities encountered. Sixty-six percent of the cases were documented as middle ear anomalies in the absence of any other evidence of congenital disease. Improved hearing was obtained in 47% of those cases where corrective surgery was undertaken. Treatment and results are reviewed. The pattern of ossicular abnormality encountered in this series suggests a variable origin of the incus, either from first branchial arch alone or from both first and second branchial arches.

摘要

回顾了68例因听小骨异常导致的先天性传导性听力损失病例。记录了每例病例的临床和手术细节,并根据所发现的异常情况制定了分类。66%的病例被记录为中耳异常,且无任何其他先天性疾病的证据。在接受矫正手术的病例中,47%的患者听力得到改善。对治疗方法和结果进行了回顾。该系列中所遇到的听小骨异常模式表明,砧骨的起源存在差异,要么仅来自第一鳃弓,要么来自第一和第二鳃弓。

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Congenital ossicular abnormalities: a review of 68 cases.先天性听小骨异常:68例病例回顾
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