Department of Cardiac Surgery, Carlo Poma Hospital, Mantua, Italy.
Perfusion. 2022 May;37(4):429-431. doi: 10.1177/0267659121999300. Epub 2021 Mar 5.
Aortic dissection during pregnancy is a very rare event in the general population but can be fatal to both the mother and the fetus. A rate of dissection as high as 10% was observed in pregnant patients affected by Marfan syndrome. Facing this kind of disease can represent a challenge for the involved physicians because of its rarity. Here we present the case of an aortic dissection in a pregnant woman with Marfan syndrome who previously underwent an open heart surgery for a mitral prolapse. The diagnosis and the treatment of this case, given the mid-term gestational age combined with an increased surgical risk due to the reintervention, required a particular effort by our team. A multidisciplinary approach to the management of this patient was the key to achieve a favorable outcome both for the mother and for the baby.
主动脉夹层在一般人群中非常罕见,但对母亲和胎儿都可能是致命的。马凡综合征患者中,夹层的发生率高达 10%。由于其罕见性,面对这种疾病可能对参与的医生构成挑战。在这里,我们介绍了一位患有马凡综合征的孕妇主动脉夹层的病例,该患者曾因二尖瓣脱垂接受过心脏直视手术。鉴于中期妊娠和再次干预引起的手术风险增加,该病例的诊断和治疗需要我们团队付出特别的努力。对该患者的管理采取多学科方法是实现母婴双方良好结局的关键。