Thuong Vu Le, Minh Duc Nguyen, Tra My Thieu-Thi, Tan Lien Bang Mai, Tuan Linh Le, Quynh Huong Tran
Department of Internal Medicine University of Medicine and Pharmacy at Ho Chi Minh City Ho Chi Minh City Vietnam.
Department of Radiology Children's Hospital 2 Ho Chi Minh City Vietnam.
Respirol Case Rep. 2021 Feb 28;9(4):e00731. doi: 10.1002/rcr2.731. eCollection 2021 Apr.
Congenital bronchobiliary fistula (CBBF) is a very rare malformation associated with clinical symptoms of dyspnoea, vomiting, cyanosis, persistent pneumonia, and poor response to antibiotics. Typical imaging techniques used to diagnose this malformation include bronchography, computed tomography (CT), cholangiography, hepatobiliary nuclear imaging, and magnetic resonance imaging (MRI). We diagnosed a case of CBBF that was initially diagnosed as non-resolving pneumonia. CT and fistulography were used to obtain the correct diagnosis. The fistula was confirmed by fistulography under the guidance of bronchoscopy. Surgical excision of the fistulous tract was performed, with complete recovery. The aim of this report was to emphasize the epidemiology and clinical features of CBBF patients.
先天性支气管胆管瘘(CBBF)是一种非常罕见的畸形,伴有呼吸困难、呕吐、发绀、持续性肺炎以及对抗生素反应不佳等临床症状。用于诊断这种畸形的典型影像学技术包括支气管造影、计算机断层扫描(CT)、胆管造影、肝胆核素显像和磁共振成像(MRI)。我们诊断了一例最初被诊断为迁延不愈肺炎的CBBF病例。通过CT和瘘管造影获得了正确诊断。在支气管镜引导下通过瘘管造影证实了瘘管的存在。对瘘管进行了手术切除,患者完全康复。本报告的目的是强调CBBF患者的流行病学和临床特征。