Department of Pediatric Cardiology, Japan Community Health Organization Chukyo Hospital, Minami-ku, Nagoya, Japan.
Department of Cardiovascular Surgery, Japan Community Health Organization Chukyo Hospital, Minami-ku, Nagoya, Japan.
Cardiol Young. 2021 Apr;31(4):644-645. doi: 10.1017/S1047951121000779. Epub 2021 Mar 8.
This is a case of a female infant with bilateral coronary ostial atresia associated with pulmonary atresia and ventricular septal defect. She developed coronary ischemia at 1-month of age, when she underwent an aortopulmonary shunt and an aorta-right ventricle shunt. The double-orifice tricuspid valve was separating the right ventricle from the left ventricle. She required extracorporeal cardiopulmonary support because of ventricular dysfunction and mitral regurgitation. Although she was temporarily weaned off the support after mitral valvuloplasty, she died from multiple organ failure. To the best of our knowledge, bilateral coronary ostial atresia associated with pulmonary atresia with ventricular septal defect has not been reported previously.
这是一例双侧冠状动脉口闭锁伴肺动脉闭锁和室间隔缺损的女性婴儿病例。她在 1 个月大时发生冠状动脉缺血，当时接受了主动脉肺动脉分流术和主动脉右心室分流术。双孔三尖瓣将右心室与左心室隔开。由于心室功能障碍和二尖瓣反流，她需要体外心肺支持。尽管在二尖瓣瓣成形术后她暂时脱离了支持，但她死于多器官衰竭。据我们所知，以前没有报道过双侧冠状动脉口闭锁伴肺动脉闭锁伴室间隔缺损。
